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Unusual Forms of Dementia

  • Chapter
Dementia

Abstract

Other chapters in this volume have analysed the common types of dementia, such as Alzheimer’s disease, vascular dementia, diffuse Lewy body disease, and so on. There remain 1–5% of patients in whom dementia is due to a wide variety of disorders, many of them rare. In many such instances, dementia represents one aspect of a complex disorder in which other neurological or systemic features usually predominate. Nevertheless, awareness of these disorders in which dementia is sometimes the presenting or dominant feature may lead to effective treatment (for example, in Wilson’s disease, or Whipple’s disease) or may influence management in other ways, such as the provision of genetic counselling. This chapter attempts to summarize the most important clinical and diagnostic aspects of some of these disorders.

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Authors
  1. J. J. M. Kew
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  2. P. N. Leigh
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Editors and Affiliations

  1. University of Manchester, UK

    Alistair Burns (Professor of Old Age Psychiatry) (Professor of Old Age Psychiatry)

  2. Institute of Psychiatry, London, UK

    Raymond Levy (Professor of Old Age Psychiatry) (Professor of Old Age Psychiatry)

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Kew, J.J.M., Leigh, P.N. (1994). Unusual Forms of Dementia. In: Burns, A., Levy, R. (eds) Dementia. Springer, Boston, MA. https://doi.org/10.1007/978-1-4615-6805-6_50

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