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Solitary Fibrous Tumor/Hemangiopericytoma

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Management of Soft Tissue Sarcoma

Abstract

Solitary fibrous tumor (SFT) can occur at any age (Fig. 11.1) and any site (Fig. 11.2). As with vascular sarcomas, solitary fibrous tumor/hemangiopericytoma (SFT/HPC) represents a spectrum of tumors ranging from well-circumscribed tumors with bland spindle-shaped cells to histologically malignant tumors with a high mitotic rate and significant risk of metastatic disease. SFT/HPC arises in the pleura, pelvis, and in the dura, where it is termed hemangiopericytoma exclusively by neuropathologists. Even among neuropathologists, there is increasing appreciation that what has been termed HPC and SFT are indeed related [1].

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Brennan, M.F., Antonescu, C.R., Maki, R.G. (2013). Solitary Fibrous Tumor/Hemangiopericytoma. In: Management of Soft Tissue Sarcoma. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-5004-7_11

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  • DOI: https://doi.org/10.1007/978-1-4614-5004-7_11

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