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Neuroanesthesia and Coexisting Genetic Problems

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Co-existing Diseases and Neuroanesthesia

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Abstract

There are ample number of neurosurgical conditions that have associated genetic disorders. Neurosurgical conditions include craniosynostosis, craniopagus twins, and craniovertebral anomalies like atlantoaxial instability, meningomyelocele, and other neural tube defects. Some of the commonly associated genetic disorders are Down’s syndrome, Klippel-Feil syndrome, Goldenhar syndrome, Apert syndrome, and Muenke syndrome. Findings vary from airway changes to bony changes and from cardiac to renal anomalies. Depending upon the type and severity of the lesions, possible complications may vary from neurologic sequelae, respiratory complications, ventilatory and weaning issues, coagulation abnormalities, positioning problems to common problems like venous air embolism, temperature and acid-base changes, and fluid and electrolyte abnormalities to postoperative pain management. Dedicated neuroanesthesia care is the key to a successful perioperative management and positive outcome of these patients.

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Author information

Authors and Affiliations

  1. Department of Anesthesia, Nizam’s Institute of Medical Sciences, Hyderabad, India

    Srilata Moningi

  2. Department of Neurosurgery, Apollo Hospitals, Hyderabad, India

    Subodh Raju

Authors
  1. Srilata Moningi
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  2. Subodh Raju
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Editors and Affiliations

  1. Department of Neuroanaesthesiology and Critical Care, All India Institute of Medical Sciences, New Delhi, India

    Hemanshu Prabhakar

  2. Department of Neuroanesthesiology and Neurocritical Care, Medanta, The Medicity, Gurugram, India

    Vasudha Singhal

  3. Department of Neuroanaesthesia, Indraprastha Apollo Hospital, New Delhi, India

    Nidhi Gupta

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Moningi, S., Raju, S. (2019). Neuroanesthesia and Coexisting Genetic Problems. In: Prabhakar, H., Singhal, V., Gupta, N. (eds) Co-existing Diseases and Neuroanesthesia. Springer, Singapore. https://doi.org/10.1007/978-981-13-2086-6_13

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  • DOI: https://doi.org/10.1007/978-981-13-2086-6_13

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  • Publisher Name: Springer, Singapore

  • Print ISBN: 978-981-13-2085-9

  • Online ISBN: 978-981-13-2086-6

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