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Role of Ultrasonography for the Diagnosis of Pancreaticobiliary Maljunction and Congenital Biliary Dilatation

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Pancreaticobiliary Maljunction and Congenital Biliary Dilatation

Abstract

PBM is one of the anomalous conditions in which the bile duct and the pancreatic duct merge outside the duodenal wall, which causes continuous pancreaticobiliary reflux (PR). PBM is classified into two groups as follows: PBM with biliary dilatation (congenital biliary dilatation, CBD) and PBM without dilatation. US must be the best method for the diagnosis of PBM associated with CBD, revealing extrahepatic or intrahepatic bile duct dilatation. In adults, the maximum inner diameter of extrahepatic bile duct (MDEBD) was recently reported. MDEBD positively correlated with age. In cases of PBM without bile duct dilatation, thickening of the gallbladder wall as a characteristic sonographic feature has been reported. Hyperplastic changes with increased cell proliferation in gallbladder mucosa induced by PR could reflect as thickening of the gallbladder. A high confluence of pancreaticobiliary ducts (HCPBD) has been defined as a disease state. In HCPBD cases, PR and hyperplastic changes in gallbladder were observed. US is an important image modality to give clues to the diagnosis in cases with PBM, CBD, and HCPBD, because it can reveal sonographic characteristics such as gallbladder wall thickening and/or mild dilatation of the extrahepatic bile duct.

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Correspondence to Keiji Hanada .

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Hanada, K., Shimizu, A., Minami, T. (2018). Role of Ultrasonography for the Diagnosis of Pancreaticobiliary Maljunction and Congenital Biliary Dilatation. In: Kamisawa, T., Ando, H. (eds) Pancreaticobiliary Maljunction and Congenital Biliary Dilatation. Springer, Singapore. https://doi.org/10.1007/978-981-10-8654-0_12

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  • DOI: https://doi.org/10.1007/978-981-10-8654-0_12

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  • Publisher Name: Springer, Singapore

  • Print ISBN: 978-981-10-8653-3

  • Online ISBN: 978-981-10-8654-0

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