Abstract
Diagnostic Criteria of Pancreaticobiliary Maljunction: Pancreaticobiliary maljunction is a congenital malformation in which the pancreatic and bile ducts join anatomically outside the duodenal wall. Pancreaticobiliary maljunction is diagnosed by either imaging test or anatomical examination. An abnormally long common channel and/or an abnormal union between the pancreatic and bile ducts must be evident on direct cholangiography such as ERCP, PTC, or intraoperative cholangiography, MRCP, or 3D-DIC-CT. The elevated amylase levels in bile and extrahepatic bile duct dilatation strongly suggest the existence of pancreaticobiliary maljunction.
Diagnostic Criteria of Congenital Biliary Dilatation: Congenital biliary dilatation is a congenital malformation involving both local dilatation of the extrahepatic bile duct, including the common bile duct, and pancreaticobiliary maljunction. However, cases associated with intrahepatic bile duct dilatation can be included in this entity. For a diagnosis of congenital biliary dilatation, both abnormal dilatation of the bile duct and pancreaticobiliary maljunction must be evident by either imaging or anatomical examination. Diagnosis of biliary dilatation must be established by using the diameter, site, and characteristic form of dilatation of the bile duct. Acquired or secondary dilatation of the bile duct, which is caused by obstruction due to biliary stones or malignancy, is strictly excluded.
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Hamada, Y. (2018). Diagnostic Criteria of Pancreaticobiliary Maljunction and Congenital Biliary Dilatation. In: Kamisawa, T., Ando, H. (eds) Pancreaticobiliary Maljunction and Congenital Biliary Dilatation. Springer, Singapore. https://doi.org/10.1007/978-981-10-8654-0_11
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