Abstract
Primary non-epithelial tumors of the pancreas are exceedingly rare. By contrast, those arising from neighboring sites, especially gastrointestinal stromal tumors and sarcomas arising from the retroperitoneum, may secondarily involve the pancreatic gland. There is also a wide range of benign mesenchymal tumors, including vascular tumors, fibromatosis (solid desmoid tumor), solitary fibrous tumors, schwannomas, and several others that can involve the pancreas. Some primary sarcomas have also been shown to have a pancreatic localization. The histologic features of these neoplasms are thus highly variable, as they include tumors of vascular origin, primitive neuroectodermal tumors, synovial sarcomas, desmoplastic small round-cell tumors [1], leiomyosarcomas, malignant fibrous histiocytomas, and others.
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Molin, M.D., Capelli, P. (2013). Primary Non-epithelial Tumors of the Pancreas. In: Pederzoli, P., Bassi, C. (eds) Uncommon Pancreatic Neoplasms. Updates in Surgery. Springer, Milano. https://doi.org/10.1007/978-88-470-2673-5_16
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DOI: https://doi.org/10.1007/978-88-470-2673-5_16
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