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Epidemiology of Moyamoya Disease

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Moyamoya Disease Update

Abstract

Moyamoya disease has a high incidence in East Asian countries, and many large-scale epidemiological surveys of this disease have been conducted in East-Asian countries such as Japan and Republic of Korea.

In the early 1970s, several surveys first reported the epidemiological features of moyamoya disease in Japan. Since 1977, a research committee on moyamoya disease, established by the Ministry of Health and Welfare, Japan (RCMJ), has studied the epidemiology of this disease, and four nationwide surveys were conducted in Japan in 1984, 1990, 1995, and 2003 [1–5]. In Republic of Korea, a survey of moyamoya disease was first conducted in 1988, and several reports on the epidemiology of this disease in Republic of Korea have been published [6, 7].

In this chapter, we will review the epidemiology of moyamoya disease by investigating data mainly from these two countries.

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References

  1. Aoki K, Handa H, Terayama K et al (1986) A nationwide epidemiological survey of intractable diseases in Japan. In: Aoki K (ed) Annual Report of Epidemiology of Intractable Diseases Research Committee. The Research Committee on Epidemiology of Intractable Diseases, Nagoya, Japan, p 9–22

    Google Scholar 

  2. Ohno Y, Yonekawa Y, Handa H et al (1987) Clinicoepidemiological features of Spontaneous Occlusion of the Circle of Willis. In: Aoki K (ed) Annual Report of Epidemiology of Intractable Diseases Research Committee. The Research Committee on Epidemiology of Intractable Diseases, Nagoya, Japan, p 29–32

    Google Scholar 

  3. Sasaki R, Suzuki S, Tamakoshi A et al (1991) Clinicoepidemiological features of Spontaneous Occlusion of the Circle of Willis from a nationwide epidemiologcal survey. In: Yanagawa H (ed) Annual Report of Epidemiology of Intractable Diseases Research Committee. The Research Committee on Epidemiology of Intractable Diseases, Tochigi, Japan, p 30–32

    Google Scholar 

  4. Wakai K, Tamakoshi A, Ikezaki K et al (1997) Epidemiological features of moyamoya disease in Japan: findings from a nationwide survey. Clin Neurol Neurosurg 99 (suppl 2):S1–5

    Article  PubMed  Google Scholar 

  5. Kuriyama S, Kusaka Y, Fujimura M et al (2008) Prevalence and clinicoepidemiological features of moyamoya disease in Japan: findings from a nationwide epidemiological survey. Stroke 39:42–47

    Article  PubMed  Google Scholar 

  6. Choi KS (1988) Moyamoya disease in Korea: a cooperative study. In: Suzuki J (ed) Advances in surgery for cerebral stroke. Springer, Tokyo, Japan, p 107–109

    Google Scholar 

  7. Han DH, Kwon OK, Byun BJ et al (2000) A co-operative study: clinical characteristics of 334 Korean patients with moyamoya disease treated at neurosurgical institutes (1976–1994). The Korean Society for Cerebrovascular Disease. Acta Neurochir (Wien) 142:1263–1273; discussion 1273–1274

    Article  CAS  Google Scholar 

  8. Baba T, Houkin K, Kuroda S (2008) Novel epidemiological features of moyamoya disease. J Neurol Neurosurg Psychiatry 79:900–904

    Article  PubMed  CAS  Google Scholar 

  9. Ikeda K, Iwasaki Y, Kashihara H et al (2006) Adult moyamoya disease in the asymptomatic Japanese population. J Clin Neurosci 13:334–338

    Article  PubMed  Google Scholar 

  10. Oki K, Hoshino H, Suzuki N et al (2008) Database count of the Research Committee on Spontaneous Occlusion of the Circle of Willis (moyamoya disease) In: Hashimoto N (ed) A summarized report of 2005–2007 of the Research Committee on Spontaneous Occlusion of the Circle of Willis (Moyamoya Disease). The Research Committee on Spontaneous Occlusion of the Circle of Willis (Moyamoya Disease) Kyoto, Japan, p 15–20

    Google Scholar 

  11. Nanba R, Kuroda S, Tada M et al (2006) Clinical features of familial moyamoya disease. Childs Nerv Syst 22:258–262

    Article  PubMed  Google Scholar 

  12. Goto Y, Yonekawa Y (1992) Worldwide distribution of moyamoya disease. Neurol Med Chir (Tokyo) 32:883–886

    Article  CAS  Google Scholar 

  13. Uchino K, Johnston SC, Becker KJ et al (2005) Moyamoya disease in Washington State and California. Neurology 65:956–958

    Article  PubMed  Google Scholar 

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Acknowledgments

This study was assisted by a research grant from the Research Committee on Spontaneous Occlusion of the Circle of Willis (Moyamoya Disease) in the Ministry of Health, Labor and Welfare, Japan.

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Correspondence to Koichi Oki .

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Oki, K., Hoshino, H., Suzuki, N. (2010). Epidemiology of Moyamoya Disease. In: Cho, BK., Tominaga, T. (eds) Moyamoya Disease Update. Springer, Tokyo. https://doi.org/10.1007/978-4-431-99703-0_4

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  • DOI: https://doi.org/10.1007/978-4-431-99703-0_4

  • Publisher Name: Springer, Tokyo

  • Print ISBN: 978-4-431-99702-3

  • Online ISBN: 978-4-431-99703-0

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