Abstract
UCTD presents as a symptom or a set of symptoms suggesting systemic connective tissue disease (SCTD) occurring together with the positivity of autoantibodies, lasting longer than 12 months. Pulmonary involvement mostly with the picture of non-specific interstitial pneumonia (NSIP) is the part of UCTD very frequently. Criteria for the diagnosis of IIP within UCTD are not strict: at least one symptom of SCTD, at least one sign of a systemic inflammatory process, predominance of hazy opacities on chest HRCT scan, and histopathological proof of NSIP. Fifty percent of patients with NSIP fulfill these criteria when compared to only 5 % of patients with a confirmed diagnosis of idiopathic pulmonary fibrosis (IPF). In our case report we are describing the patient fulfilling these diagnostic criteria but having the less frequent histopathologic pattern of UIP.
Access this chapter
Tax calculation will be finalised at checkout
Purchases are for personal use only
Bibliography
Corte TJ, Copley SJ, Desai SR, Zapala CJ, Hansell DM, Nicholson AG, Colby TV, Renzoni E, Maher TM, Wells AU (2012) Significance of connective tissue disease features in idiopathic interstitial pneumonia. Eur Respir J 39:661–668
Tzelepis GE, Toya SP, Moutsopoulos HM (2008) Occult connective tissue diseases mimicking idiopathic interstitial pneumonias. Eur Respir J 31:11–20
Author information
Authors and Affiliations
Corresponding author
Editor information
Editors and Affiliations
Rights and permissions
Copyright information
© 2014 Springer-Verlag Wien
About this chapter
Cite this chapter
Vašáková, M. (2014). Undifferentiated Connective Tissue Disease (UCTD). In: Rovenský, J., Herold, M., Vašáková, M. (eds) Sine Syndromes in Rheumatology. Springer, Vienna. https://doi.org/10.1007/978-3-7091-1541-1_6
Download citation
DOI: https://doi.org/10.1007/978-3-7091-1541-1_6
Published:
Publisher Name: Springer, Vienna
Print ISBN: 978-3-7091-1540-4
Online ISBN: 978-3-7091-1541-1
eBook Packages: MedicineMedicine (R0)