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Operationspflichtige fetale Fehlbildungen: Pränataldiagnostik und perinatales Management

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Kinderchirurgie

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Zusammenfassung

Gute Geburtshilfe hat eine gesunde und glückliche Mutter und ein gesundes und zufriedenes Kind zum Ziel. Das perinatale Management fetaler Fehlbildungen hat das mittel- und langfristig bestmögliche Outcome für das Kind zum Ziel. Bereits pränatal sollten Fachärzte aller Disziplinen involviert werden, die voraussichtlich nach der Geburt die Fehlbildungen klinisch versorgen werden. Dies ist besonders bei gleichzeitigem Vorliegen von Fehlbildungen mehrerer Organsysteme geboten. Für ein interdisziplinäres Perinatalzentrum der Maximalversorgung (z.B. Medizinische Hochschule Hannover) sind u. a. erforderlich: Neonatologen, Kinderchirurgen, Kinderkardiologen und pädiatrische Intensivmediziner, Kinderkardiochirurgen, ECMO-Spezialisten, Kinder-Nephrologen und -Hepatologen, pädiatrische Transplantationsspezialisten, plastische Chirurgen, Mund-Kiefer-Gesichts-Chirurgen und Neurochirurgen. Dieses Kapitel beschreibt pränatale Bildgebung, Genetik, Pathophysiologie, pathologische Anatomie sowie Vorschläge für das Management der Geburt für relevante fetale Fehlbildungen.

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Author information

Authors and Affiliations

  1. Klinik für Frauenheilkunde und Geburtshilfe, Medizinische Hochschule Hannover, Hannover, Deutschland

    Constantin S. von Kaisenberg

  2. Klinik für Pädiatrische Pneumologie, Allergologie und Neonatologie, Medizinische Hochschule Hannover, Hannover, Deutschland

    Bettina Bohnhorst

  3. Klinik für Pädiatrische Kardiologie und Pädiatrische Intensivmedizin, Medizinische Hochschule Hannover, Hannover, Deutschland

    Philipp Beerbaum

Authors
  1. Constantin S. von Kaisenberg
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  2. Bettina Bohnhorst
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  3. Philipp Beerbaum
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Corresponding author

Correspondence to Constantin S. von Kaisenberg .

Editor information

Editors and Affiliations

  1. Kinderchirurgische Klinik und Poliklinik im Dr. von Haunerschen Kinderspital, LMU München, München, Germany

    Dietrich von Schweinitz

  2. Klinik für Kinderchirurgie, Medizinische Hochschule Hannover (MHH), Hannover, Germany

    Benno Ure

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von Kaisenberg, C.S., Bohnhorst, B., Beerbaum, P. (2019). Operationspflichtige fetale Fehlbildungen: Pränataldiagnostik und perinatales Management. In: von Schweinitz, D., Ure, B. (eds) Kinderchirurgie. Springer Reference Medizin. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-58202-2_11

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  • DOI: https://doi.org/10.1007/978-3-662-58202-2_11

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