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Gangliosidoses

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Lipids and Lipidoses

Abstract

The term gangliosides* was introduced by Klenk for neuraminic acid-containing glycolipids which he found (1939—1942) in the brains of subjects with infantile amaurotic family idiocy. The neuraminic acid content of gangliosides permitted differentiation from other carbohydrate-containing lipids such as cere-brosides which accumulate in Gaucher’s disease.

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Authors
  1. G. Schettler
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  2. W. Kahlke
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Schettler, G., Kahlke, W. (1967). Gangliosidoses. In: Schettler, G. (eds) Lipids and Lipidoses. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-87367-6_8

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  • DOI: https://doi.org/10.1007/978-3-642-87367-6_8

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