Abstract
Macular telangiectasia type 2 (MacTel type 2) is a disease of unknown cause with characteristic alterations of the macular capillary network and neurosensory atrophy. By the use of microperimetry for mapping functional changes, deep paracentral scotomata have been identified as a characteristic functional consequence of the disease process. Structure-function correlation revealed well-defined progressive focal photoreceptor loss to be the underlying cause for functional loss in MacTel type 2. Therefore, the increase of paracentral scotomata with time determined by microperimetry testing may represent a suitable functional outcome parameter for future interventional clinical trials.
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© 2014 Springer-Verlag Berlin Heidelberg
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Heeren, T.F.C., Holz, F.G., Issa, P.C. (2014). Macular Telangiectasia Type 2. In: Midena, E. (eds) Microperimetry and Multimodal Retinal Imaging. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-40300-2_11
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DOI: https://doi.org/10.1007/978-3-642-40300-2_11
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