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Oesophageal Atresia Associations

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Esophageal and Gastric Disorders in Infancy and Childhood

Abstract

Almost half of infants born with oesophageal atresia have an associated malformation. The most common anomaly involves the cardiovascular system affected in around 30 % of cases, followed by the gastrointestinal tract (28 %), genitourinary tract (14 %) and vertebral/limb defects (10 %).

A number of “syndromes” include oesophageal atresia among the combination of anomalies and include particularly the VACTERL association, CHARGE association and Potter’s syndrome.

Oesophageal atresia occurs sporadically in a number of other syndromes.

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Author information

Authors and Affiliations

  1. Institute of Child Health, University College, London, UK

    Lewis Spitz

  2. Great Ormond Street Hospital for Children, London, UK

    Lewis Spitz

Authors
  1. Lewis Spitz
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Correspondence to Lewis Spitz .

Editor information

Editors and Affiliations

  1. Medical University of Graz, Graz, Austria

    Holger Till

  2. Sheffield Children’s Hospital, Paediatric Gastroenterology Centre, Sheffield, United Kingdom

    Mike Thomson

  3. Division of Cardiothoracic Surgery, Department of Surgery, University of Minnesota Medical School, Minneapolis, Minnesota, USA

    John E. Foker

  4. Department Surgery, University of Missouri, Kansas City Children’s Mercy Hospital, Kansas City, Missouri, USA

    George W. Holcomb III

  5. University of Arizona, Tucson, Arizona, USA

    Khalid M. Khan

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Spitz, L. (2017). Oesophageal Atresia Associations. In: Till, H., Thomson, M., Foker, J., Holcomb III, G., Khan, K. (eds) Esophageal and Gastric Disorders in Infancy and Childhood. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-11202-7_8

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  • DOI: https://doi.org/10.1007/978-3-642-11202-7_8

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  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-11201-0

  • Online ISBN: 978-3-642-11202-7

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