Abstract
Primary bone tumors in children are rare conditions, the upper limb being more rarely affected than the lower limb. The practicing general orthopedic surgeon may not see more than a single case of primary bone tumor per year. This rarity makes the recognition— particularly of malignant bone tumors—extremely difficult. Not surprisingly, this leads to difficulties and errors being made in specific treatment. With the establishment of bone tumor/cancer registries, the incidence of malignant primary disease of bone can be seen to be around six cases per million per year. The incidence of osteosarcoma, the most common primary malignant bone tumor, showing peak risks of incidence related to puberty is greatest between 10 and 14 years for girls and between 15 and 18 years for boys [1] (Fig. 16.1).
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Cannon, S.R. (2008). Bone Tumors: Limb Salvage. In: Carachi, R., Grosfeld, J.L., Azmy, A.F. (eds) The Surgery of Childhood Tumors. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-29734-5_16
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