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Dietary Copper and Diet Issues for Patients with Wilson Disease

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Management of Wilson Disease

Part of the book series: Clinical Gastroenterology ((CG))

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Abstract

Copper is a mineral essential to human health being integral to critical biological pathways including red blood cell formation, immune function, and bone health. For those with (WD), the inability to excrete excess copper changes the way we consider dietary copper intake. There is much debate over the role of diet in Wilson disease (WD), with some health professionals proposing strict lower copper diets and others completely discounting the role of diet in treatment. So what information should we provide WD patients on optimal dietary intake at diagnosis? The following chapter presents a proposal for moderation of dietary copper intake with individualization on a case-by-case basis. In addition to impact on food intake, nutrition has other roles in management of WD. Special considerations need to be given to patients who have advanced liver disease or neurological involvement or who need supplements or nutrition support. The role of nutrition in these cases will be explored, and recommendations will be provided.

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Authors and Affiliations

  1. Department of Food and Nutrition, Yale New Haven Hospital, New Haven, CT, USA

    Anne Marie Rivard

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  1. Anne Marie Rivard
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Correspondence to Anne Marie Rivard .

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Editors and Affiliations

  1. Yale New Haven Transplantation Center, Yale University, New Haven, Connecticut, USA

    Michael L. Schilsky

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Rivard, A.M. (2018). Dietary Copper and Diet Issues for Patients with Wilson Disease. In: Schilsky, M. (eds) Management of Wilson Disease . Clinical Gastroenterology. Humana Press, Cham. https://doi.org/10.1007/978-3-319-91527-2_4

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  • DOI: https://doi.org/10.1007/978-3-319-91527-2_4

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  • Publisher Name: Humana Press, Cham

  • Print ISBN: 978-3-319-91526-5

  • Online ISBN: 978-3-319-91527-2

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