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Can Surgeons Preserve Right Ventricular Function in Hypoplastic Left Heart Syndrome?

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Right Ventricular Physiology, Adaptation and Failure in Congenital and Acquired Heart Disease

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Abstract

The systemic right ventricle in hypoplastic left heart syndrome commonly shows gradually declining function after initial palliation. It is therefore crucial to optimally preserve myocardial performance. Decisions in the operating room can have long term impact on systemic right ventricular function. For example, the choice of surgical procedures, shunt types, myocardial protection strategies, techniques used to reconstruct the hypoplastic aorta, and tricuspid valve procedures may all play an important role in the preservation of myocardial function. We herein discuss assets and drawbacks of surgical decisions with regard to right ventricular function in hypoplastic left heart syndrome, summarize currently available data, and give a perspective on contemporary and future therapy.

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Authors and Affiliations

  1. Cardiovascular Surgery, The Hospital for Sick Children, 555 University Ave, Toronto, ON, Canada, M5G 1X8

    Christoph Haller & Christopher A. Caldarone

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  1. Christoph Haller
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  2. Christopher A. Caldarone
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Correspondence to Christopher A. Caldarone .

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  1. Paediatric Cardiology, Labatt Family Heart Center Hospital for Sick Children, Toronto, Ontario, Canada

    Mark K. Friedberg

  2. Heart Institute, Cincinnati Children’s Hosp Med Center, Cincinnati, Ohio, USA

    Andrew N. Redington

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Haller, C., Caldarone, C.A. (2018). Can Surgeons Preserve Right Ventricular Function in Hypoplastic Left Heart Syndrome?. In: Friedberg, M., Redington, A. (eds) Right Ventricular Physiology, Adaptation and Failure in Congenital and Acquired Heart Disease. Springer, Cham. https://doi.org/10.1007/978-3-319-67096-6_18

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  • DOI: https://doi.org/10.1007/978-3-319-67096-6_18

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  • Online ISBN: 978-3-319-67096-6

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