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Robin Sequence

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Cleft Lip and Palate Treatment

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Abstract

Robin sequence (RS) is a congenital condition characterized by micrognathia, glossoptosis, and upper airway obstruction. Consensus was reached that micrognathia is the primary characteristic of RS. Other mandatory diagnostic characteristics include glossoptosis and airway obstruction. Cleft palate is considered a common and additional feature (Breugem and Evans 2016). The incidence of RS in the general population is 1/8500–1/14000 live births (Bush and Williams 1983; Printzlau and Andersen 2004) (Fig. 15.1).

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Authors and Affiliations

  1. Divisao de Cirurgia Plastica e Queimaduras, Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo, São Paulo, Brazil

    Nivaldo Alonso M.D., Ph.D.

  2. Department of Craniofacial Surgery, Hospital for Rehabilitation of Craniofacial Anomalies, University of São Paulo, São Paulo, Brazil

    Cristiano Tonello M.D., Ph.D. & Ilza Lazarini Marques M.D., Ph.D.

  3. Department of Plastic Surgery, University of São Paulo Hospital, São Paulo, Brazil

    Arturo Frick Carpes M.D., Ph.D.

  4. Department of Plastic Surgery, Baylor College of Medicine, Houston, TX, USA

    Marco Maricevich M.D.

  5. Department of Plastic Surgery, Texas Children’s Hospital – Baylor College of Medicine, Houston, TX, USA

    Renata Maricevich M.D.

Authors
  1. Nivaldo Alonso M.D., Ph.D.
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  2. Cristiano Tonello M.D., Ph.D.
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  3. Ilza Lazarini Marques M.D., Ph.D.
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  4. Arturo Frick Carpes M.D., Ph.D.
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  5. Marco Maricevich M.D.
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  6. Renata Maricevich M.D.
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Correspondence to Nivaldo Alonso M.D., Ph.D. .

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Editors and Affiliations

  1. University of São Paulo Medical School, São Paulo, São Paulo, Brazil

    Nivaldo Alonso

  2. SOBRAPAR Hospital, Campinas, São Paulo, Brazil

    Cassio Eduardo Raposo-Amaral

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Alonso, N., Tonello, C., Marques, I.L., Carpes, A.F., Maricevich, M., Maricevich, R. (2018). Robin Sequence. In: Alonso, N., Raposo-Amaral, C. (eds) Cleft Lip and Palate Treatment. Springer, Cham. https://doi.org/10.1007/978-3-319-63290-2_15

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  • DOI: https://doi.org/10.1007/978-3-319-63290-2_15

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