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Status Epilepticus in the Idiopathic Generalized Epilepsies

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Status Epilepticus

Part of the book series: Current Clinical Neurology ((CCNEU))

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Abstract

Status epilepticus in the idiopathic generalized epilepsies (IGE-SE) may take three forms: generalized convulsive (IGE-GCSE), typical absence status (IGE-AS), and myoclonic status (IGE-MSE). This chapter critically reviews the position of all types of IGE-SE in the new International League Against Epilepsy (ILAE) proposal on status classification, its epidemiology, pathophysiology, clinical symptoms, emergency electroencephalography (EEG) features, diagnosis and differential diagnosis, and briefly, its treatment. IGE-AS and IGE-MSE are examined in all IGE sub-syndromes with particular emphasis on clinical and EEG semiology and precipitants, including treatment with anti-seizure drugs (ASD) that are appropriate for IGE. Pertinent points include: (1) no IGE sub-syndrome is immune to IGE-AS or MSE, but clinical and EEG semiology and incidence commonly appear to be syndrome-related; (2) episodes can be related to, or triggered by, use of anti-seizure drugs inappropriate for use in IGE; (3) episodes mostly appear responsive to appropriate treatment and management; (4) recurrent episodes are not only related to poor compliance and unsuitable life styles, or associated with inappropriate ASDs, but may also reflect late unexplained adverse evolution of an IGE syndrome previously in remission, or be a predominant or defining seizure-symptom in particular IGE sub-syndromes.

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  1. Department of Clinical Neurophysiology and Epilepsies, St Thomas’ Hospital, Guy’s & St Thomas’ NHS Foundation Trust, Westminster Bridge Road, London, SE1 7EH, UK

    Michail Koutroumanidis

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  1. Michail Koutroumanidis
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Correspondence to Michail Koutroumanidis .

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  1. Department of Neurology, Harvard Medical School, Comprehensive Epilepsy Center, Beth Israel Deaconess Medical Center, Boston, Massachusetts, USA

    Frank W. Drislane

  2. Department of Neurology, Johns Hopkins Bayview Medical Center, Baltimore, Maryland, USA

    Peter W. Kaplan MBBS

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Koutroumanidis, M. (2018). Status Epilepticus in the Idiopathic Generalized Epilepsies. In: Drislane, F., Kaplan MBBS, P. (eds) Status Epilepticus. Current Clinical Neurology. Springer, Cham. https://doi.org/10.1007/978-3-319-58200-9_15

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  • DOI: https://doi.org/10.1007/978-3-319-58200-9_15

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  • Print ISBN: 978-3-319-58198-9

  • Online ISBN: 978-3-319-58200-9

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