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Primary Cutaneous Marginal Zone Lymphoma

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Atlas of Cutaneous Lymphomas

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Abstract

Primary cutaneous marginal zone lymphoma (pcMZL) is an indolent B-cell lymphoma that commonly presents with red to violaceous plaques, nodules, or tumors. It has an excellent prognosis. This entity has also been known as cutaneous marginal zone lymphoma (CMZL), extranodal marginal zone lymphoma of mucosa associated lymphoid tissue (MZL or MALT lymphoma), primary cutaneous immunocytoma, primary cutaneous plasmacytoma, and lymphoma cutis [1, 2]. This chapter will discuss the clinical presentation, prognosis, treatment, histopathology, immunophenotype, and differential diagnosis of pcMZL. It closes with a clinical case, including clinical images and histopathology.

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Authors and Affiliations

  1. Harvard-MIT Division of Health Sciences and Technology, Harvard Medical School, Boston, MA, USA

    Amrita Goyal M.D.

  2. Department of Dermatology, Massachusetts General Hospital, Harvard Medical School, Boston, MA, USA

    Joi B. Carter M.D.

  3. Comprehensive Cutaneous Lymphoma Program, Department of Medicine, Massachusetts General Hospital Cancer Center, Boston, MA, USA

    Jeffrey A. Barnes M.D., Ph.D.

  4. Dermatopathology Service, Department of Pathology, Massachusetts General Hospital, Harvard Medical School, Boston, MA, USA

    Lyn McDivitt Duncan M.D.

Authors
  1. Amrita Goyal M.D.
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  2. Joi B. Carter M.D.
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  3. Jeffrey A. Barnes M.D., Ph.D.
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  4. Lyn McDivitt Duncan M.D.
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Correspondence to Lyn McDivitt Duncan M.D. .

Editor information

Editors and Affiliations

  1. Department of Dermatology, Massachusetts General Hospital, Boston, Massachusetts, USA

    Joi B. Carter

  2. Division of Health Sciences and Technology, Harvard Medical School, Boston, Massachusetts, USA

    Amrita Goyal

  3. Dermatopathology Service, Massachusetts General Hospital, Boston, Massachusetts, USA

    Lyn McDivitt Duncan

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Goyal, A., Carter, J.B., Barnes, J.A., Duncan, L.M. (2015). Primary Cutaneous Marginal Zone Lymphoma. In: Carter, J., Goyal, A., McDivitt Duncan, L. (eds) Atlas of Cutaneous Lymphomas. Springer, Cham. https://doi.org/10.1007/978-3-319-17217-0_16

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  • DOI: https://doi.org/10.1007/978-3-319-17217-0_16

  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-17216-3

  • Online ISBN: 978-3-319-17217-0

  • eBook Packages: MedicineMedicine (R0)

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