Abstract
Biliary hamartomas result from abnormal embryologic development of the ductal plate. They are the most common variant of fibropolycystic liver disease, which includes also Caroli disease, choledochal cysts, polycystic liver disease, and congenital hepatic fibrosis. They are also called von Meyenburg complexes, and typically are small cystic lesions (less than 1.5 cm), encountered as an incidental finding on imaging exams. The gold standard for the diagnosis is magnetic resonance, which demonstrates the cystic lesions in the intrahepatic biliary tree. Usually, they are benign lesions, and the risk of malignancy is extremely rare.
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Motta, R., Pirazzini, A., Lupi, A., Marchesi, P., Giraudo, C., Floreani, A. (2021). Biliary Hamartomas. In: Floreani, A. (eds) Diseases of the Liver and Biliary Tree. Springer, Cham. https://doi.org/10.1007/978-3-030-65908-0_3
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