Abstract
Genodermatoses with malignant potential often manifest cutaneous findings as the presenting feature (Table 1). In most cases, the diagnosis can be made by clinical criteria or genetic testing. Prompt diagnosis is critical to initiate appropriate screening for malignancy.
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Abbreviations
- APC:
-
Adenomatous polyposis coli
- BCC:
-
Basal cell carcinoma
- BCCNS:
-
Basal cell carcinoma nevus syndrome
- FAP:
-
Familial adenomatous polyposis
- HLRCC:
-
Hereditary leiomyomatosis and renal cell cancer
- MEN:
-
Multiple endocrine neoplasia
- MPNST:
-
Malignant peripheral nerve sheath tumor
- MTS:
-
Muir-Torre syndrome
- NF:
-
Neurofibroma
- TS:
-
Tuberous sclerosis
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Hernandez Holt, M., Liu, V., Dyer, J. (2021). Genodermatoses with Malignant Potential. In: Liu, V. (eds) Dermato-Oncology Study Guide. Springer, Cham. https://doi.org/10.1007/978-3-030-53437-0_3
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DOI: https://doi.org/10.1007/978-3-030-53437-0_3
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