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Hypogonadisme hypogonadotrophique congénital: procréation, grossesses et descendance

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Pathologie hypophysaire et grossesse

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Les hypogonadismes hypogonadotrophiques congénitaux sont une cause ďinsuffisance de développement pubertaire et ďinfertilité chez la femme et chez ľhomme (1). Ils résultent de la sécrétion insuffisante de gonadotrophines hypophysaires, LH et/ou FSH. Le traitement de ľinfertilité chez les hommes et les femmes est une demande habituelle des patients avec HHC après le traitement de ľhypogonadisme. Il pose actuellement, dans certaines étiologies, le problème de la transmission de la maladie à la descendance et génère une activité croissante de conseil génétique, de surveillance des grossesses induites médicalement et de prise en charge diagnostique et thérapeutique du nouveau-né.

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Young, J. (2007). Hypogonadisme hypogonadotrophique congénital: procréation, grossesses et descendance. In: Pathologie hypophysaire et grossesse. Springer, Paris. https://doi.org/10.1007/978-2-287-35572-1_11

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  • DOI: https://doi.org/10.1007/978-2-287-35572-1_11

  • Publisher Name: Springer, Paris

  • Print ISBN: 978-2-287-35571-4

  • Online ISBN: 978-2-287-35572-1

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