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Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia

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Clinical Approach to Sudden Cardiac Death Syndromes

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Abstract

Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is a genetically determined heart muscle disease that predominantly affects the right ventricle (RV).1-4 It is characterized pathologically by myocardial atrophy and fibrofatty replacement of the right ventricular myocardium, and clinically by right ventricular electrical instability, leading to ventricular tachycardia (VT) or ventricular fibrillation (VF), which may precipitate sudden cardiac arrest mostly in young people and athletes.1-6 Later, in the natural history, the RV may become more diffusely involved and the left ventricle progressively affected with subsequent biventricular heart failure.4,5

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Authors and Affiliations

  1. Department of Cardiac, Thoracic and Vascular Sciences, University of Padua Medical School, Via Giustiniani, 2, 35121, Padua, Italy

    Domenico Corrado (Professor of Cardiovascular Medicine)

Authors
  1. Michela Bevilacqua
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  2. Federico Migliore
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  3. Cristina Basso
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  4. Gaetano Thiene
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  5. Domenico Corrado
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Corresponding author

Correspondence to Domenico Corrado .

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Editors and Affiliations

  1. Masonic Medical Research Laboratory, Bleecker St. 2150, Utica, 13501, U.S.A.

    Ramon Brugada

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Bevilacqua, M., Migliore, F., Basso, C., Thiene, G., Corrado, D. (2010). Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia. In: Brugada, R. (eds) Clinical Approach to Sudden Cardiac Death Syndromes. Springer, London. https://doi.org/10.1007/978-1-84882-927-5_13

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  • DOI: https://doi.org/10.1007/978-1-84882-927-5_13

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  • Online ISBN: 978-1-84882-927-5

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