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Hirschsprung Disease

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Pediatric Neurogastroenterology

Part of the book series: Clinical Gastroenterology ((CG))

Abstract

Over the past century dramatic advances have been made in Hirschsprung disease diagnosis, surgical management, developmental biology, and genetics. Ongoing studies provide new hope that we will be able to reduce HSCR incidence, prevent HAEC, replace missing enteric neurons using stem cells, image the ENS intra-operatively, improve surgical techniques, and incorporate genetics into clinical practice.

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Authors and Affiliations

  1. Department of Pediatrics, Division of Gastroenterology, Hepatology, and Nutrition, Washington University School of Medicine, 660 South Euclid Avenue, 8208, St. Louis, MO, 63110, USA

    Robert O. Heuckeroth M.D., Ph.D

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  1. Robert O. Heuckeroth M.D., Ph.D
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Correspondence to Robert O. Heuckeroth M.D., Ph.D .

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Editors and Affiliations

  1. Sainte-Justine Hospital, Department of Pediatrics, Division of Pediatric Gastroenterology, Université de Montréal, Montreal, H3T 1C5, Québec, Canada

    Christophe Faure

  2. Nationwide Children's Hospital, Division of Pediatric Gastroenterology, The Ohio State University, Columbus, 43205, Ohio, USA

    Carlo Di Lorenzo

  3. Gastroenterology and Neural Development, University College London, Institute of Child Health, Great Ormond Street Hospital for Children, London, WC1N 1EH, United Kingdom

    Nikhil Thapar

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Heuckeroth, R.O. (2013). Hirschsprung Disease. In: Faure, C., Di Lorenzo, C., Thapar, N. (eds) Pediatric Neurogastroenterology. Clinical Gastroenterology. Humana Press, Totowa, NJ. https://doi.org/10.1007/978-1-60761-709-9_23

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  • DOI: https://doi.org/10.1007/978-1-60761-709-9_23

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