Abstract
Lesions that differentiate toward skeletal muscle form a distinct subgroup of soft tissue tumors. They include a small number of benign tumors and tumor-like lesions and a clinically more important group of malignant neoplasms: rhabdomyosarcomas. Although they are uncommon overall, rhabdomyosarcomas of embryonal and alveolar types, which are genetically distinct, are the most frequent soft tissue sarcomas of childhood and adolescence. Pleomorphic rhabdomyosarcoma occurs mainly in older adults. Spindle cell rhabdomyosarcoma has two forms: the pediatric type, which is relatively indolent, and the adult type, which is a more aggressive neoplasm.
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Fisher, C. (2013). Skeletal Muscle Tumors. In: Atlas of Soft Tissue Tumor Pathology. Atlas of Anatomic Pathology. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-7025-0_12
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DOI: https://doi.org/10.1007/978-1-4614-7025-0_12
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