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Abstract

Vascular anomalies are classified into vascular tumors and vascular malformations based on the classification system of the International Society for the Study of Vascular Anomalies (ISSVA) [1, 2]. Vascular tumors are characterized by proliferation and tumor enlargement, and the most common vascular tumor is infantile hemangioma, while a less common vascular tumor is hemangiopericytoma. Vascular malformations consist of non-proliferating vascular lesions in which blood flow is misdirected through anomalous channels. Malformations exist on a spectrum, ranging from high-flow arteriovenous malformation (AVM), low-flow venous (varix) and lymphovenous malformations, and capillary-venous malformations. Flow characteristics influence the natural history of vascular anomalies and are helpful in making the correct diagnosis.

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Correspondence to Alon Kahana M.D., Ph.D. .

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Kahana, A. (2012). Orbital Vascular Anomalies. In: Black, E., Nesi, F., Calvano, C., Gladstone, G., Levine, M. (eds) Smith and Nesi’s Ophthalmic Plastic and Reconstructive Surgery. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-0971-7_61

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  • DOI: https://doi.org/10.1007/978-1-4614-0971-7_61

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