Abstract
Cystic Fibrosis (CF) is a lethal hereditary disorder affecting approximately 1 in 1500 Caucasian births in the United States (Bowman & Mango, 1976). It presents a special challenge to the pediatric health care community because of the lethality, complexity, and unknown cause of the disease. CF may affect several organ systems, including respiratory, gastrointestinal (GI), pancreas, kidney, and reproduction (Matthews & Drotar, 1984). The exocrine glands of these various organ systems produce an abnormal mucus that is thick, viscous, and sticky. The most serious complications of the disease involves abnormal mucus production in the lungs and pancreas.
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© 1990 Plenum Press, New York
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Stark, L.J., Spirito, A., Hobbs, S.A. (1990). The Role of Behavior Therapy in Cystic Fibrosis. In: Gross, A.M., Drabman, R.S. (eds) Handbook of Clinical Behavioral Pediatrics. Applied Clinical Psychology. Springer, Boston, MA. https://doi.org/10.1007/978-1-4613-0505-7_15
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DOI: https://doi.org/10.1007/978-1-4613-0505-7_15
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