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Defining Terms in Lists of Nomenclature

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Pediatric and Congenital Cardiac Care

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Abstract

A hierarchical organization of terms with definitions for pediatric and congenital heart disease (PCHD) comprises a language or system of communication that can be used to accurately describe the diagnoses and procedures associated with developmental cardiac malformations as well as acquired cardiac diseases that affect children and may persist into adulthood. However, some of the existing terminology is regional, disorganized, redundant, ambiguous and imprecise. As such, an internationally accepted, cohesive and comprehensive set of terms with definitions for PCHD is required to unify the subspecialty. To achieve this goal, the mission of the Definitions Working Group (DWG) of the International Society for the Nomenclature of Pediatric and Congenital Heart Disease (ISNPCHD) is to create scientifically accurate, precise and concise definitions for all of the diagnostic and procedural terms encompassed by the International Paediatric and Congenital Cardiac Code (IPCCC). A hierarchy and definitions for many of the parent terms of the IPCCC will also be used to populate the PCHD terms for the upcoming International Classification of Diseases (ICD-11) published by the World Health Organization (WHO). The ongoing work of the DWG ultimately has the potential to create a universally accepted, cohesive and comprehensive set of terms for PCHD with scientifically accurate and clear definitions. The ultimate realization of this goal would greatly facilitate and improve international PCHD outcomes analyses and quality improvement strategies.

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Authors and Affiliations

  1. Department of Cardiovascular Surgery, Children’s Hospital of Michigan, FTA, Wayne State University School of Medicine, 3901 Beaubien Boulevard, Detroit, MI, 48201, USA

    Henry L. Walters III MD

  2. Department of Cardiology, Boston Children’s Hospital, 300 Longwood Avenue, Boston, MA, 02115, USA

    Steven D. Colan MD, FAHA, FACC, FASE

Authors
  1. Henry L. Walters III MD
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  2. Steven D. Colan MD, FAHA, FACC, FASE
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Correspondence to Henry L. Walters III MD .

Editor information

Editors and Affiliations

  1. School of Medicine,, University of Oslo, Oslo, Norway

    Paul R. Barach

  2. Division of Cardiac Surgery, Department of Surgery, Johns Hopkins University, Division of Cardiac Surgery, Department of Surgery, Johns Hopkins All Children’s Heart Institute, All Children’s Hospital and Florida Hospital for Children, Johns Hopkins University, St. Petersburg, Tampa, Orlando, FL, USA,, Baltimore, Maryland, USA

    Jeffery P. Jacobs

  3. Wayne State University, Detroit, Michigan, USA

    Steven E. Lipshultz

  4. The Hospital for Sick Children, Toronto, Ontario, Canada

    Peter C. Laussen

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Walters, H.L., Colan, S.D. (2015). Defining Terms in Lists of Nomenclature. In: Barach, P., Jacobs, J., Lipshultz, S., Laussen, P. (eds) Pediatric and Congenital Cardiac Care. Springer, London. https://doi.org/10.1007/978-1-4471-6587-3_6

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  • DOI: https://doi.org/10.1007/978-1-4471-6587-3_6

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  • Publisher Name: Springer, London

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  • Online ISBN: 978-1-4471-6587-3

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