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Sinus of Valsalva Aneurysm and Fistula

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Comprehensive Approach to Adult Congenital Heart Disease

Abstract

This anomaly forms due to a lack or a separation between the aortic wall media and the aortic valveā€™s annulus fibrosus. The delivery cardiac chamber of a right aortic sinus fistula is typically the right ventricle. However, infrequently, when there is noncoronary cusp involvement, the right atrium becomes the drainage location. The left aortic sinus is rarely involved. Related abnormalities consist of ventricular septal defect, bicuspid aortic valve, and coarctation of the aorta [1, 2].

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References

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Correspondence to Anita Sadeghpour MD, FACC, FASE .

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Video 39.1

Transthoracic echocardiography in short axis view showing aneurysmal dilation of right sinus of Valsalva with protrusion to the RVOT (AVI 4942 kb)

Transesophageal echocardiography in short axis view revealed a ā€œwindsockā€ dilatation of the right sinus of Valsalva which is ruptured to the RA and color flow imaging showing continuous systolic-diastolic flow (MPG 2606 kb)

Transesophageal echocardiography in short axis view revealed a ā€œwindsockā€ dilatation of the right sinus of Valsalva which is ruptured to the RA and color flow imaging showing continuous systolic-diastolic flow (MPG 2308 kb)

Video 39.4

Transesophageal echocardiography in long axis view revealed a ā€œwindsockā€ dilatation of the right sinus of Valsalva which is ruptured to the RVOT (white arrow) and associated VSD (yellow arrow) and color flow imaging showing continuous turbulent systolic-diastolic flow drains to the RVOT (AVI 2145 kb)

Transesophageal echocardiography in long axis view revealed a ā€œwindsockā€ dilatation of the right sinus of Valsalva which is ruptured to the RVOT (white arrow) and associated VSD (yellow arrow) and color flow imaging showing continuous turbulent systolic-diastolic flow drains to the RVOT (AVI 3903 kb)

Aortic root injection revealed rupture sinus of Valsalva to the right ventricle (MPG 3650 kb)

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Sadeghpour, A., Alizadehasl, A. (2014). Sinus of Valsalva Aneurysm and Fistula. In: Sadeghpour, A., Kyavar, M., Alizadehasl, A. (eds) Comprehensive Approach to Adult Congenital Heart Disease. Springer, London. https://doi.org/10.1007/978-1-4471-6383-1_39

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  • DOI: https://doi.org/10.1007/978-1-4471-6383-1_39

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  • Publisher Name: Springer, London

  • Print ISBN: 978-1-4471-6382-4

  • Online ISBN: 978-1-4471-6383-1

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