Abstract
Atrioventricular septal defect (AVSD) consists of a group of anomalies with the common main pathology of the absence of the atrioventricular (AV) septum associated with the abnormalities of the AV valves [1]. AVSD has been divided into the two main categories as the partial and complete forms and two other subtypes as the transitional (which is the subtype of partial AVSD) and intermediate (which is the subtype of complete AVSD). In complete AVSD, a primum ASD is concomitant with an inlet-type ventricular septal defect (VSD), and a common AV valve has only single annulus. In addition, transitional AVSD is used when a partial AVSD also has a small inlet-type VSD that is partially obstructed via chordal attachments to the intraventricular septum. Also, intermediate subtype of AVSD has separate right and left AV valve orifices even though having only one common annulus. These distinct orifices are referred to as right and left AV valve orifices rather than mitral and tricuspid [2, 3].
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References
Bonow RO, Mann DL, Zipes DP, Libby P, eds. Braunwald’s Heart Disease: A Textbook of Cardiovascular Medicine. 9th ed. Philadelphia, PA: Saunders Elsevier; 2011.
Gatzoulis MA, Webb GD, Broberg CS, Uemura H. Cases in adult congenital heart disease. Philadelphia: Churchill Livingstone; 2010.
Warnes C, Williams RG, Bashore TM, et al. ACC/AHA, guidelines for the management of adults with congenital heart disease. J Am Coll Cardiol. 2008;52(23):e143–263.
Warnes CA. Adult congenital heart disease, American Heart Association. AHA clinical series. Wiley Blackwell; 2009. Chapter 2. p. 9–24.
Allen HD, Driscoll DJ, Shady RE. Moss and Adams’ heart disease in infants, children, and adolescents: including the fetus and young adults. 7th ed. Philadelphia: Lippincott Williams & Wilkins; 2008.
Eidem BW, Cetta F, O’leary PW. Echocardiography in pediatric and adult congenital heart disease. Philadelphia: Lippincott Williams & Wilkins; 2012.
Aubert S, Henaine R, Raisky O, et al. Atypical forms of isolated partial atrioventricular septal defect increase the risk of initial valve replacement and reoperation. Eur J Cardiothorac Surg. 2005;28:223–8.
Bergin ML, Warnes CA, Tajik AJ, et al. Partial atrioventricular canal defect: long-term follow-up after initial repair in patients >40 years old. J Am Coll Cardiol. 1995;25:1189–94.
McGrath LB, Gonzalez-Lavin L. Actuarial survival, freedom from reoperation, and other events after repair of atrioventricular septal defects. J Thorac Cardiovasc Surg. 1987;94:582.
Vet TW, Ottenkamp J. Correction of atrioventricular septal defect. Results influenced by Down syndrome? Am J Dis Child. 1989;143(11):1361–5.
Carpentier A. Surgical anatomy and management of the mitral component of atrioventricular canal defects. In: Anderson RH, Shinebourne EA, editors. Paediatric cardiology. Edinburgh: Churchill Livingstone; 1978. p. 477–90.
Piccoli GP, Wilkinson JL, Macartney FJ, et al. Morphology and classification of complete atrioventricular defects. Br Heart J. 1979;42:633–9.
Atz AM, Hawkins JA, Lu M, et al. Surgical management of complete atrioventricular septal defect: associations with surgical technique, age, and trisomy 21. J Thorac Cardiovasc Surg. 2011;141(6):1371–9.
Nicholson IA, Nunn GR, Sholler GF, et al. Simplified single patch technique for the repair of atrioventricular septal defect. J Thorac Cardiovasc Surg. 1999;118(4):642–6.
Drenthen W, Pieper PG, van der Tuuk K, et al. Cardiac complications relating to pregnancy and recurrence of disease in the offspring of women with atrioventricular septal defects. Eur Heart J. 2005;26:2581–7.
Drenthen W, Pieper PG, Roos-Hesselink JW, et al. Outcome of pregnancy in women with congenital heart disease. J Am Coll Cardiol. 2007;49:2303–11.
Calabrò R, Limongelli G. Complete atrioventricular canal. Orphanet J Rare Dis. 2006;1:8.
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Complete AVSD with a common AV valve, large ostium primum type atrial septal defect’ and large inlet type inter-ventricular septum defect (WMV 281 kb)
Complete AVSD with common AV valve and it’s five leaflets (superior bridging, left mural, inferior bridging, right mural and right antero-superior leaflets) (WMV 394 kb)
Video 23.3
Complete AVSD, Rastelli Type A, the superior bridging leaflet is attached to the crest of ventricular septum (MPG 790 kb)
Complete AVSD, Rastelli Type C in short axis and 4 chamber views, the superior bridging leaflet is attached to the papillary muscle on RV free wall (WMV 294 kb)
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Alizadehasl, A., Sadeghpour, A., Akiash, N. (2014). Atrioventricular Septal Defect (AVSD). In: Sadeghpour, A., Kyavar, M., Alizadehasl, A. (eds) Comprehensive Approach to Adult Congenital Heart Disease. Springer, London. https://doi.org/10.1007/978-1-4471-6383-1_23
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DOI: https://doi.org/10.1007/978-1-4471-6383-1_23
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