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Histiocytosis and Storage Diseases

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Dail and Hammar’s Pulmonary Pathology

Abstract

Histiocytoses of the lung include a variety of diseases for which the unifying characteristic is the accumulation of histiocytic cells within lung parenchyma or air spaces. The diseases include macrophage and dendritic cell disorders as well as storage diseases that result in the accumulation of histiocytic cells in the lung. Pulmonary Langerhans’ cell histiocytosis is the most common of these disorders. The histologic, radiologic, immunohistochemical, and, where relevant, ultrastructural characteristics of these diseases are compared in Table 16.1 and discussed in the various sections of this chapter.

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Authors and Affiliations

  1. Harrison Medical Center, Pathology Associates of Kitsap County, Bremerton, WA, 98310, USA

    Samuel P. Hammar MD

  2. Department of Pathology, University of Texas Health Center at Tyler, Tyler, TX, 75708, USA

    Timothy C. Allen MD, JD (Chairman)

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Editors and Affiliations

  1. Department of Pathology, Case Western Reserve University School of Medicine, Cleveland, OH, USA

    Joseph F. Tomashefski Jr. MD (Professor and Chairman) (Professor and Chairman)

  2. Department of Pathology, MetroHealth Medical Center, Cleveland, OH, USA

    Joseph F. Tomashefski Jr. MD (Professor and Chairman) (Professor and Chairman)

  3. Department of Pathology, Weill Medical College of Cornell University, New York, NY

    Philip T. Cagle MD (Professor and Director) (Professor and Director)

  4. Pulmonary Pathology, Department of Pathology, The Methodist Hospital, Houston, TX, USA

    Philip T. Cagle MD (Professor and Director) (Professor and Director)

  5. Pulmonary Pathology, Department of Anatomic Pathology, The Cleveland Clinic Foundation, Cleveland, OH, USA

    Carol F. Farver MD (Director) (Director)

  6. Department of Pathology, University of Massachusetts Medical School, Worcester, MA, USA

    Armando E. Fraire MD (Professor) (Professor)

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Hammar, S.P., Allen, T.C. (2008). Histiocytosis and Storage Diseases. In: Tomashefski, J.F., Cagle, P.T., Farver, C.F., Fraire, A.E. (eds) Dail and Hammar’s Pulmonary Pathology. Springer, New York, NY. https://doi.org/10.1007/978-0-387-68792-6_16

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