Abstract
An 18-years-old male presented to emergency department after a car accident with the diagnosis of femoral bone fracture. Arterial blood pressure was 160/90 mmHg in both arms. Bilateral femoral and popliteal pulses were extremely weak and there was systolic ejection murmur on the left second intercostals area. Chest X-ray showed rib notching with normal cardiac silhouette. Transthoracic echocardiography showed the aortic interruption just below the left subclavian artery. Aortography showed a complete interruption of the aortic arch (IAA) just distal to the origin of the left subclavian artery. Femoral bone fracture was treated by conservative strategy. A gadolinium contrast-enhanced magnetic resonance angiogram (1.5 T scanners) clearly reaffirmed a complete interruption of the descending aorta, 3.6 cm from the left subclavian artery with extensive collateralizations. Mild degree hypertension was controlled by a long acting calcium channel blocker. Later the patient has been scheduled for elective surgical repair. We aimed to discuss the diagnostic and treatment options of the interrupted aortic arch as being a rare anomaly.
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References
Backer CL, Mavroudis C.Congenital Heart Surgery Nomenclature and Database Project:patent ductus arteri-osus,coarctation of the aorta,interrupted aortic arch.Ann Thorac Surg 2000;69(4 Suppl):S298–S307.
Canova CR, Carrel T, Dubach P, Turina M, Reinhart WH. Interrupted aortic arch:fortuitous diagnosis in a 72-year old female patient with severe aortic insufficiency.Schweiz Med Wochenschr 1995;125(1–2):26–30.
Collins-Nakai RL, Dick M, Parisi-Buckley L, Fyler DC, Castaneda AR.Interrupted aortic arch in infancy.J Pediatr 1976;88:959–962.
Messner G, Reul GJ, Flamm SD, Gregoric ID, Opfermann UT.Interrupted aortic arch in an adult,single-stage extra-anatomic repair.Tex Heart Inst J 2002;29:118–121.
Steidele RJ.Samml Chir u Med Beob (Vienna)1778;2:114.
Celoria GC, Patton RB.Congenital absence of the aortic arch.Am Heart J 1959;58:407–413.
Smallhorn JF, Anderson RH, Macartney FJ.Cross-sectional echocardiograhic recognition of interruption of aortic arch between the left carotid artery and subclavien arteries. Br Heart J 1982;48:229–235.
Roche KJ, Glenn K, Vivian SL, Neil R, Nancy B.Inter-rupted aortic arch:diagnosis with Gadolinium-enhanced 3D MRA.J Comput Assist Tomogr 1999;23(2):197–202.
Varghese A, Gatzoulis M, Mohiaddin RH.Magnetic Res-onance Angiography of a Congenitally Interrupted Aortic Arch.Circulation 2002;106:e9–e10.
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Akdemir, R., Ozhan, H., Erbilen, E. et al. Isolated Interrupted Aortic Arch: A Case Report and Review of the Literature. Int J Cardiovasc Imaging 20, 389–392 (2004). https://doi.org/10.1023/B:CAIM.0000041940.14780.1c
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DOI: https://doi.org/10.1023/B:CAIM.0000041940.14780.1c