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Bilateral Aldosterone-Producing Adrenocortical Carcinoma: a Rare Entity

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Indian Journal of Surgical Oncology Aims and scope Submit manuscript

Abstract

Adrenal cortical carcinomas (ACC) are rare aggressive malignant neoplasms with a reported incidence of 1–2 cases per 1 million population and account for 0.05–0.2 % of all malignancies. About 60 % are functional tumors and majority, 40 % present with Cushing’s syndrome. Rarely, 2.5 to 11 % present with hypertension due to increased secretion of aldosterone and are usually unilateral. Bilateral aldosterone-producing adrenocortical carcinoma (APAC) has not been reported yet. We report a case of bilateral APAC in a 22-year-old male.

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Acknowledgments

Bombay Hospital

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Authors and Affiliations

  1. Department of Surgical Oncology, Bombay Hospital, Bombay hospital Marg, Marine Drive, Mumbai, Maharashtra, 400020, India

    Garima Daga & Sanjay Sharma

  2. Minimal Invasive Urology, Department of Urology and Kidney Transplant, Medanta, The Medicity, Gurgaon, Haryana, 122001, India

    Varun Mittal

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  1. Garima Daga
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  2. Sanjay Sharma
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  3. Varun Mittal
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Correspondence to Garima Daga.

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The authors declare that they have no conflict of interest.

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Daga, G., Sharma, S. & Mittal, V. Bilateral Aldosterone-Producing Adrenocortical Carcinoma: a Rare Entity. Indian J Surg Oncol 8, 88–90 (2017). https://doi.org/10.1007/s13193-016-0563-8

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  • DOI: https://doi.org/10.1007/s13193-016-0563-8

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