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Présentation insolite d’un sarcome embryonnaire indifférencié du foie : à propos d’un cas

Unusual presentation of an undifferentiated embryonal sarcoma of the liver: a case report

  • Cas Clinique / Case Report
  • Published:
Journal Africain d'Hépato-Gastroentérologie

Résumé

Le sarcome embryonnaire indifférencié du foie est une tumeur rare survenant à la fin de l’enfance. Cette tumeur est caractérisée par une présentation clinique et radiologique souvent trompeuse. Nous rapportons un cas de sarcome embryonnaire hépatique primaire chez une jeune fille de 15 ans pris à tort pour un kyste hydatique du foie rompu et nous discutons ses caractéristiques anatomo-cliniques, thérapeutiques et évolutives.

Abstract

Undifferentiated embryonal sarcoma of the liver is a rare tumor occurring in late childhood. This tumor is often characterized by a misleading clinical and radiological presentation. We report a case of primary hepatic embryonal sarcoma in a 15 years old girl erroneously assumed to be a rupture hydatic cyst and discuss its clinicopathologic, therapeutic and evolutive features.

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Authors and Affiliations

  1. Service d’oncologie médicale CHU Habib Bourguiba, Sfax, Tunisie

    W. Boukettaya, N. Toumi, A. Khanfir & M. Frikha

  2. Service de chirurgie générale CHU Habib Bourguiba, Sfax, Tunisie

    A. Ghorbel & M. I. Bayrouti

  3. Service de chirurgie générale Hôpital Mongi Slim, La Marsa, Tunisie

    H. Mestiri

  4. Service d’anatomopathologie CHU Habib Bourguiba, Sfax, Tunisie

    T. Boudawara

Authors
  1. W. Boukettaya
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  2. N. Toumi
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  3. A. Khanfir
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  4. A. Ghorbel
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  5. H. Mestiri
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  6. T. Boudawara
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  7. M. I. Bayrouti
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  8. M. Frikha
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Correspondence to W. Boukettaya.

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Boukettaya, W., Toumi, N., Khanfir, A. et al. Présentation insolite d’un sarcome embryonnaire indifférencié du foie : à propos d’un cas. J Afr Hepato Gastroenterol 8, 97–99 (2014). https://doi.org/10.1007/s12157-014-0526-z

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  • DOI: https://doi.org/10.1007/s12157-014-0526-z

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