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Chondromyxoid Fibroma of Sphenoid Sinus with Unusual Calcifications: Case Report with Literature Review

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Abstract

Chondromyxoid fibroma (CMF) is a rare benign primary tumor which usually affects the metaphyses of the long bone of the lower extremities in childhood and young adults. Rarely, CMF occurs in the skull base and parasinuses, which may be difficult to distinguish from chondrosarcoma or chordoma and other tumors in the head. It is composed of chondroid, myxoid, and fibrous tissue growth in a lobular pattern, infrequently with calcifications. We report one case of CMF involving the sphenoid sinus mimicking a chondrosarcoma. The tumor mass showed calcifications on images and histology.

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Acknowledgments

The authors thank Dr. Michael Klein from Hospital for Special Surgery and Dr. German Steiner from Hospital for Joint Disease, for their reviewing this case and providing their expertise to make the diagnosis.

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Authors and Affiliations

  1. Department of Otolaryngology, New York University School of Medicine, 550 First Avenue, HCC-3C, New York, NY, 10016, USA

    Luc G. T. Morris, Jordan Rihani & Richard A. Lebowitz

  2. Department of Pathology, New York University School of Medicine, 550 First Avenue, TCH-461, New York, NY, 10016, USA

    Beverly Y. Wang

Authors
  1. Luc G. T. Morris
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  2. Jordan Rihani
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  3. Richard A. Lebowitz
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  4. Beverly Y. Wang
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Correspondence to Beverly Y. Wang.

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Morris, L.G.T., Rihani, J., Lebowitz, R.A. et al. Chondromyxoid Fibroma of Sphenoid Sinus with Unusual Calcifications: Case Report with Literature Review. Head and Neck Pathol 3, 169–173 (2009). https://doi.org/10.1007/s12105-009-0121-6

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  • DOI: https://doi.org/10.1007/s12105-009-0121-6

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