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Childhood Electroclinical Syndromes: A Diagnostic and Therapeutic Algorithm

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Abstract

Childhood Electroclinical Syndromes (CES) are epilepsies occurring in childhood with certain common features such as age of onset, types of seizures, electroencephalographic (EEG) characteristics, response to antiepileptic drugs (AEDs) and outcome. An understanding of CES is important for proper management and counseling. There are several CES, and there is an ongoing debate about lumping vs. splitting the CES. For the uninitiated, it is a difficult task to remember all the CES. In this paper, a simplified pragmatic diagnostic and therapeutic algorithm for some of the common CES is presented.

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Abbreviations

CLON:

Clonic

TON:

Tonic

TCS:

Tonic Clonic Seizure

MYO:

Myoclonic

ATO:

Atonic

ABS:

Absence

SPS:

Simple Partial Seizures

CPS:

Complex Partial Seizures

CBZ:

Carbamazepine

PHT:

Phenytoin

VAL:

Valproate

PB:

Phenobarbitone

OXC:

Oxcarbazepine

LTG:

Lamotrigine

TPM:

Topiramate

GBP:

Gabapentine

ESM:

Ethosuximide

ZM:

Zonisamide

ACTH:

Adreno-corticotrophic hormone

CLB:

Clobazam

RUF:

Rufinamide

N:

Normal

Abn:

Abnormal

S:

Spikes

PS:

Polyspikes

SW:

Spike Waves

PSW:

Polyspike wave

GEN:

Generalized discharges

F:

Focal

HV:

Hyperventilation

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Authors and Affiliations

  1. Pediatric Neurology and Neurodevelopment Unit, Department of Pediatrics, Advanced Pediatrics Centre, Post Graduate Institute of Medical Education and Research, Chandigarh, 160012, India

    Pratibha Singhi

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  1. Pratibha Singhi
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Singhi, P. Childhood Electroclinical Syndromes: A Diagnostic and Therapeutic Algorithm. Indian J Pediatr 81, 888–897 (2014). https://doi.org/10.1007/s12098-014-1529-x

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  • DOI: https://doi.org/10.1007/s12098-014-1529-x

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