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An extremely rare case of unilateral renal arterial and venous multiple deformity, combined with duplex pelvis and malrotation

  • Urology - Case Report
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Abstract

Renal vascular deformity (RVD) happens during the embryonic period when kidneys ascend into the lumber region. However, the exact etiology of this deformity remains unknown. RVD is not a rare congenital anomaly in urology as many cases with vascular deformity have been reported.However, no case has been reported with unilateral kidney almost in the normal position, but with several different branches of ectopic arteries—one even receiving the arterial supply from the contralateral iliac artery—and ectopic veins, one of which forms a collateral circulation with the portal vein. Moreover, it is quite interesting that this case of RVD is combined with another abnormality—duplex pelvis and renal malrotation. We will present this extremely rare case of multiple malformation of the right renal vascular deformity combined with duplex pelvis and malrotation.

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Acknowledgments

This paper was supported by the Pillar Program from Science and Technology Department of Sichuan Province (Grant No. 2012SZ0009).

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Authors and Affiliations

  1. Department of Urology, West China Hospital, Sichuan University, No. 37 Guoxue Xiang, Chengdu, 610041, China

    Liang Gao, Siyuan Bu, Fan Wan, Qiang Wei, Ping Han, Tianyong Fan & Lu Yang

  2. Department of Radiology, West China Hospital, Sichuan University, No. 37 Guoxue Xiang, Chengdu, 610041, China

    Fei Zhao

Authors
  1. Liang Gao
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  2. Siyuan Bu
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  3. Fan Wan
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  4. Fei Zhao
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  5. Qiang Wei
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  6. Ping Han
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  7. Tianyong Fan
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  8. Lu Yang
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Corresponding authors

Correspondence to Tianyong Fan or Lu Yang.

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Gao, L., Bu, S., Wan, F. et al. An extremely rare case of unilateral renal arterial and venous multiple deformity, combined with duplex pelvis and malrotation. Int Urol Nephrol 45, 327–332 (2013). https://doi.org/10.1007/s11255-013-0388-0

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  • DOI: https://doi.org/10.1007/s11255-013-0388-0

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