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Ciliated hepatic foregut cysts in children

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Abstract

Ciliated hepatic foregut cyst (CHFC) is a rare foregut developmental malformation usually diagnosed in adulthood; however, rare cases have been reported in the pediatric population. CHFC can transform into a squamous cell carcinoma resulting in death despite surgical resection of the isolated malignancy. We report the presentation, evaluation, and surgical management of a symptomatic 17-year-old girl found to have a 6.5 × 4.5 cm CHFC and suggest that all patients with suspected CHFC undergo prompt evaluation and complete cyst excision.

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Acknowledgments

We would like to thank Aaron Shaver, MD (Department of Pathology) for providing the histopathology photographs. This study was supported in part by the National Research Service Award T32HS013833 (VZ) from the Agency of Healthcare Research and Quality, and by the National Institute of Diabetes and Digestive and Kidney Disease Training Grant 2T32DK007673-13 (MR); both from the National Institutes of Health and US Department of Health and Human Services.

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Authors and Affiliations

  1. Department of Surgery, Monroe Carell Jr. Children’s Hospital at Vanderbilt University, Nashville, TN, USA

    Victor Zaydfudim, Harold N. Lovvorn III, C. Wright Pinson & Burnett S. Kelly Jr.

  2. Division of Pediatric Gastroenterology, Hepatology and Nutrition, Monroe Carell Jr. Children’s Hospital at Vanderbilt University, Nashville, TN, USA

    Michael J. Rosen & Lynette A. Gillis

  3. Department of Pathology, Monroe Carell Jr. Children’s Hospital at Vanderbilt University, Nashville, TN, USA

    Hernan Correa

  4. Division of Hepatobiliary Surgery and Liver Transplant, Vanderbilt University Medical Center, 1313 21st Avenue South, 801 Oxford House, Nashville, TN, 37232-4753, USA

    Burnett S. Kelly Jr.

Authors
  1. Victor Zaydfudim
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  2. Michael J. Rosen
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  3. Lynette A. Gillis
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  4. Hernan Correa
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  5. Harold N. Lovvorn III
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  6. C. Wright Pinson
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  7. Burnett S. Kelly Jr.
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Correspondence to Burnett S. Kelly Jr..

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Zaydfudim, V., Rosen, M.J., Gillis, L.A. et al. Ciliated hepatic foregut cysts in children. Pediatr Surg Int 26, 753–757 (2010). https://doi.org/10.1007/s00383-009-2468-x

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  • DOI: https://doi.org/10.1007/s00383-009-2468-x

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