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Rosette-forming glioneuronal tumor outside the fourth ventricle: a case-based update

  • Case-Based Update
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Abstract

Introduction

Rosette-forming glioneuronal tumors (RGNTs) that do not involve the fourth ventricle are rare. RGNTs were originally thought to be exclusively localized into the fourth ventricle but were found in various anatomical localizations.

Material and methods

We review the literature and found 32 cases of this particular RGNT. The outcome was excellent with no mortality reported after surgical treatment. Only two patients had received adjuvant therapy for progression. We added one case of a RGNT located in the cerebellar hemisphere.

Case and conclusion

She underwent a subtotal removal with no evidence of progression after. This WHO grade I tumor with a specific biphasic histopathology is of a good oncological outcome after surgical treatment. A long follow-up is needed as recurrence or metastatic progressions exist.

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Authors and Affiliations

  1. Department of Pediatric Neurosurgery, Necker-Enfants Malades Hospital, 149 Rue de Sèvres, 75015, Paris, France

    Pierre-Aurelien Beuriat & Federico Di Rocco

  2. Department of Pediatric Neurosurgery, Neurological and Neurosurgical Hospital Pierre Wertheimer, 59 Boulevard Pinel, 69677, Lyon Cedex, France

    Pierre-Aurelien Beuriat & Federico Di Rocco

  3. Department of Neuropathology, Sainte-Anne Hospital, 75674, Paris, Cedex 14, France

    Arnault Tauziede-Espariat, Melanie Pages & Pascalae Varlet

  4. Paris Descartes University, 12 Rue de l’École de Médecine, 75006, Paris, France

    Melanie Pages & Pascalae Varlet

Authors
  1. Pierre-Aurelien Beuriat
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  2. Arnault Tauziede-Espariat
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  3. Melanie Pages
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  4. Pascalae Varlet
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  5. Federico Di Rocco
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Correspondence to Pierre-Aurelien Beuriat.

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Beuriat, PA., Tauziede-Espariat, A., Pages, M. et al. Rosette-forming glioneuronal tumor outside the fourth ventricle: a case-based update. Childs Nerv Syst 32, 65–68 (2016). https://doi.org/10.1007/s00381-015-2922-0

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  • DOI: https://doi.org/10.1007/s00381-015-2922-0

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