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Expanded endonasal endoscopic approach for resection of a large skull base aneurysmal bone cyst in a pediatric patient with extensive cranial fibrous dysplasia

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Abstract

Aneurysmal bone cysts (ABCs) are uncommon non-neoplastic, hemorrhagic, and expansile osseous lesions. These lesions most commonly occur in the first two decades of life and affect the long bones and spinal column. Skull base involvement is rare. The authors report the case of a 16-year-old boy who presented with acute visual decline and was found to have a large skull base ABC centered in the sphenoid sinus. In addition, the patient had extensive cranial fibrous dysplasia. The patient underwent a staged expanded endonasal endoscopic approach for complete resection of this lesion with excellent return of his vision. This case adds to the growing body of evidence supporting a role for expanded endonasal endoscopic procedures in pediatric patients with skull base pathologies.

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Acknowledgments

We thank Dr. Allison McCoy for her help and obtaining the patient’s visual fields.

Disclosure

The authors declare that they have no conflicts of interest.

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Authors and Affiliations

  1. Department of Neurosurgery, Johns Hopkins Hospital, Baltimore, MD, 21287, USA

    Vafi Salmasi & Gary L. Gallia

  2. Department of Radiology, Johns Hopkins Hospital, Baltimore, MD, USA

    Ari M. Blitz

  3. Department of Otorhinolaryngology, Johns Hopkins Hospital, Baltimore, MD, USA

    Masaru Ishii

Authors
  1. Vafi Salmasi
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  2. Ari M. Blitz
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  3. Masaru Ishii
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  4. Gary L. Gallia
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Correspondence to Gary L. Gallia.

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Salmasi, V., Blitz, A.M., Ishii, M. et al. Expanded endonasal endoscopic approach for resection of a large skull base aneurysmal bone cyst in a pediatric patient with extensive cranial fibrous dysplasia. Childs Nerv Syst 27, 649–656 (2011). https://doi.org/10.1007/s00381-010-1341-5

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  • DOI: https://doi.org/10.1007/s00381-010-1341-5

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