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Benign fibrous hamartoma of infancy: a case of MR imaging paralleling histologic findings

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Abstract

Fibrous hamartoma of infancy is a rare fibrous tumor of the subcutaneous tissue in infants. While most case reports focus on the unique histologic appearance, which has traditionally been relied upon for diagnosis, there are few reports in the radiology literature of its appearance at MR imaging. In this report, the authors present the case of a 9-month-old male who presented with a soft tissue mass on the shoulder. The MRI findings in benign fibrous hamartoma of infancy parallel the three components of the lesion seen histologically, with an organized arrangement of fat interspersed among heterogeneous soft tissue bands composed of mesenchymal and fibrous tissue. When present, this characteristic appearance may allow the diagnosis to be suggested preoperatively.

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Conflict of interest

The authors declare that they have no conflicts of interest.

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Authors and Affiliations

  1. Department of Radiology, University of Virginia, PO Box 800170, Charlottesville, VA, 22908, USA

    J. D. Stensby & N. C. Nacey

  2. Department of Pathology, University of Virginia, PO Box 800904, Charlottesville, VA, 22908, USA

    M. R. Conces

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  1. J. D. Stensby
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  2. M. R. Conces
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  3. N. C. Nacey
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Correspondence to N. C. Nacey.

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Stensby, J.D., Conces, M.R. & Nacey, N.C. Benign fibrous hamartoma of infancy: a case of MR imaging paralleling histologic findings. Skeletal Radiol 43, 1639–1643 (2014). https://doi.org/10.1007/s00256-014-1940-4

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  • DOI: https://doi.org/10.1007/s00256-014-1940-4

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