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Interstitial Lung Disease in a Child with Antisynthetase Syndrome

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Abstract

Introduction

Antisynthetase Syndrome is associated with interstitial lung disease in adult patients, but this has not been described in children.

Materials and methods

A 13-year-old with interstitial lung disease due to Antisynthetase Syndrome and pulmonary arterial hypertension underwent emergent bilateral lung transplantation after a rapid clinical decline.

Conclusion

We present the clinical, radiographic, and histological findings of a child with interstitial lung disease due to Antisynthetase Syndrome.

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Conflict of interest

The authors have no conflict of interest or disclosures related to any companies or organizations whose products or services discussed in this manuscript.

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Authors and Affiliations

  1. Department of Pediatrics, The Ohio State University College of Medicine, Nationwide Children’s Hospital, 700 Children’s Drive, Columbus, 43205, OH, USA

    Don Hayes Jr. & Mark E. Peeples

  2. Department of Pathology, The Ohio State University College of Medicine, Nationwide Children’s Hospital, Columbus, OH, USA

    Peter B. Baker & Kathleen K. Nicol

  3. Department of Pharmaceutical Sciences, University of Kentucky College of Pharmacy, Lexington, KY, USA

    Heidi M. Mansour

Authors
  1. Don Hayes Jr.
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  2. Peter B. Baker
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  3. Heidi M. Mansour
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  4. Mark E. Peeples
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  5. Kathleen K. Nicol
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Corresponding author

Correspondence to Don Hayes Jr..

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Hayes, D., Baker, P.B., Mansour, H.M. et al. Interstitial Lung Disease in a Child with Antisynthetase Syndrome. Lung 191, 441–443 (2013). https://doi.org/10.1007/s00408-013-9468-2

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  • DOI: https://doi.org/10.1007/s00408-013-9468-2

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