Lung

, Volume 191, Issue 4, pp 441–443

Interstitial Lung Disease in a Child with Antisynthetase Syndrome

Authors

    • Department of PediatricsThe Ohio State University College of Medicine, Nationwide Children’s Hospital
  • Peter B. Baker
    • Department of PathologyThe Ohio State University College of Medicine, Nationwide Children’s Hospital
  • Heidi M. Mansour
    • Department of Pharmaceutical SciencesUniversity of Kentucky College of Pharmacy
  • Mark E. Peeples
    • Department of PediatricsThe Ohio State University College of Medicine, Nationwide Children’s Hospital
  • Kathleen K. Nicol
    • Department of PathologyThe Ohio State University College of Medicine, Nationwide Children’s Hospital
Article

DOI: 10.1007/s00408-013-9468-2

Cite this article as:
Hayes, D., Baker, P.B., Mansour, H.M. et al. Lung (2013) 191: 441. doi:10.1007/s00408-013-9468-2

Abstract

Introduction

Antisynthetase Syndrome is associated with interstitial lung disease in adult patients, but this has not been described in children.

Materials and methods

A 13-year-old with interstitial lung disease due to Antisynthetase Syndrome and pulmonary arterial hypertension underwent emergent bilateral lung transplantation after a rapid clinical decline.

Conclusion

We present the clinical, radiographic, and histological findings of a child with interstitial lung disease due to Antisynthetase Syndrome.

Keywords

Antisynthetase syndromeAnti-Jo-1 antibodyChildInterstitial lung disease

Copyright information

© Springer Science+Business Media New York 2013