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Segmental Odontomaxillary Dysplasia: Report of 3 Cases and Literature Review

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Abstract

Segmental Odontomaxillary Dysplasia (SOD) is an uncommon developmental disorder of unknown etiology that causes a unilateral alteration of the maxilla associated with an abnormal growth and maturation of bone, lack of one or both premolars and delayed tooth eruption on the affected side, alteration of adjacent gingival tissue with or without facial cutaneous lesions. Radiographically is observed an irregular trabecular pattern and reduction of the maxillary sinus. There are 50 cases reported in the English-language literature. A literature review is herein presented emphasizing the clinical, radiographic, and histological features, and three additional cases of SOD affecting a 22 years-old woman, a 18 years-old man, and a 5 years-old boy, respectively are described.

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Authors and Affiliations

  1. Oral Diagnosis Department, Semiology and Oral Pathology, Piracicaba Dental School, State University of Campinas (UNICAMP), Piracicaba, Sao Paulo, Brazil

    Wilfredo Alejandro González-Arriagada, Pablo Agustin Vargas & Marcio Ajudarte Lopes

  2. Oral Pathology and Diagnosis, Facultad de Odontología, Universidad de Valparaíso, Valparaiso, Chile

    Wilfredo Alejandro González-Arriagada, Rodrigo Fuentes-Cortés & Marco Antonio Nasi-Toso

  3. Área de Semiologia, Faculdade de Odontologia de Piracicaba-UNICAMP, Av. Limeira, 901, Bairro Areão, Piracicaba, São Paulo, CEP: 13.414-903, Brazil

    Marcio Ajudarte Lopes

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  1. Wilfredo Alejandro González-Arriagada
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  2. Pablo Agustin Vargas
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  3. Rodrigo Fuentes-Cortés
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  4. Marco Antonio Nasi-Toso
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  5. Marcio Ajudarte Lopes
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Correspondence to Marcio Ajudarte Lopes.

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González-Arriagada, W.A., Vargas, P.A., Fuentes-Cortés, R. et al. Segmental Odontomaxillary Dysplasia: Report of 3 Cases and Literature Review. Head and Neck Pathol 6, 171–177 (2012). https://doi.org/10.1007/s12105-011-0315-6

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  • DOI: https://doi.org/10.1007/s12105-011-0315-6

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