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Neuromuscular hamartoma of the trigeminal nerve in an adult

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Summary

A 36-year-old female presented with a long-standing history of headache. Computed tomography scan and magnetic resonance imaging revealed an enhancing lesion occupying the right Meckel’s cave, enlarging the trigeminal ganglion and extending through the foramen ovale into the infratemporal fossa. A right frontotemporal extradural approach to the cavernous sinus was performed and a firm, pinkish lesion intermingled with nerve fibers enlarging the trigeminal ganglion and V3 branch was identified. Frozen section was suggestive of a neuromuscular hamartoma. The lesion was sub-totally resected to avoid injury to the motor branch.

Neuromuscular hamartoma should be included in the differential diagnosis of cavernous sinus and cranial nerve lesions in adults.

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Authors and Affiliations

  1. Department of Neurosurgery, Cleveland Clinic Foundation, Cleveland, Ohio, USA

    S. Tobias, C.-H. Kim, B. Sade & J. H. Lee

  2. Brain Tumor Institute, Cleveland Clinic Foundation, Cleveland, Ohio, USA

    S. Tobias, C.-H. Kim, B. Sade & J. H. Lee

  3. Department of Anatomic Pathology, Cleveland Clinic Foundation, Cleveland, Ohio, USA

    S. M. Staugaitis

Authors
  1. S. Tobias
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  2. C.-H. Kim
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  3. B. Sade
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  4. S. M. Staugaitis
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  5. J. H. Lee
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Tobias, S., Kim, CH., Sade, B. et al. Neuromuscular hamartoma of the trigeminal nerve in an adult. Acta Neurochir (Wien) 148, 83–87 (2006). https://doi.org/10.1007/s00701-005-0642-z

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  • DOI: https://doi.org/10.1007/s00701-005-0642-z

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