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Diagnosis and Management of Budd Chiari Syndrome: An Update

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Abstract

Imaging plays a crucial role in the early detection and assessment of the extent of disease in Budd Chiari syndrome (BCS). Early diagnosis and intervention to mitigate hepatic congestion is vital to restoring hepatic function and alleviating portal hypertension. Interventional radiology serves a key role in the management of these patients. The interventionist should be knowledgeable of the clinical presentation as well as key imaging findings, which often dictate the approach to treatment. This article concisely reviews the etiology, pathophysiology, and clinical presentation of BCS and provides a detailed description of imaging and treatment options, particularly interventional management.

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Acknowledgments

Megan Griffiths assisted with the editing and formatting of images for this manuscript.

Conflict of interest

Alexander Copelan, Erick M. Remer, Mark Sands, Hanh Nghiem, and Baljendra Kapoor declare that they have no conflict of interest.

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Authors and Affiliations

  1. Diagnostic Radiology Department, William Beaumont Hospital, 3601 W 13 Mile Rd., Royal Oak, MI, 48073, USA

    Alexander Copelan & Hanh Nghiem

  2. Imaging Institute, Cleveland Clinic, 9500 Euclid Ave. A21, Cleveland, OH, USA

    Erick M. Remer

  3. Imaging Institute, Cleveland Clinic, 9500 Euclid Ave. L10, Cleveland, OH, USA

    Mark Sands & Baljendra Kapoor

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  1. Alexander Copelan
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Correspondence to Alexander Copelan.

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Copelan, A., Remer, E.M., Sands, M. et al. Diagnosis and Management of Budd Chiari Syndrome: An Update. Cardiovasc Intervent Radiol 38, 1–12 (2015). https://doi.org/10.1007/s00270-014-0919-9

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