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SPENCD Presenting with Evans Phenotype and Clinical Response to JAK1/2 Inhibitors—a Report of 2 Cases

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Fig. 1

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References

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Acknowledgements

The authors thank Dr. Zinet Currimbhoy who started the Immunology Department at B. J. Wadia Hospital for Children in the early 2000s and continues to support and mentor the department.

COE Consortium

Vaishnavi V. Iyengara#, Sangeeta Mudaliarb, Manisha R. Madkaikarc, Minnie Bodhanwalad

aDepartment of Paediatric Immunology, B. J. Wadia Hospital for Children, Mumbai, India

bDepartment of Paediatric Haematology and Oncology, B. J. Wadia Hospital for Children, Mumbai, India

cDepartment of Immunology and Leukocyte Biology, ICMR—National Institute of Immunohematology (NIIH), Parel, Mumbai, India

dDepartment of Paediatrics, B. J. Wadia Hospital for Children, Mumbai, India

#Consortium representative

Author information

Authors and Affiliations

  1. Department of Paediatric Immunology, B. J. Wadia Hospital for Children, Acharya Donde Marg, Parel, Mumbai, 400012, India

    Akshaya Chougule, Prasad Taur, Vijaya Gowri & Mukesh M. Desai

Authors
  1. Akshaya Chougule
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  2. Prasad Taur
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  3. Vijaya Gowri
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  4. Mukesh M. Desai
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Consortia

C. O. E. Consortium

  • Vaishnavi V. Iyengar
  • , Sangeeta Mudaliar
  • , Manisha R. Madkaikar
  •  & Minnie Bodhanwala

Contributions

AC: compilation and analysis of data, drafting and revision of manuscript. PT, VG: clinical management of case, data collection and analysis. MMD: conceptualization and supervision of study, interpretation of data, critical revision of manuscript. COE Consortium—VVI: clinical management of case, data collection and analysis; MRM: immunological workup; SM, MB: supervision of the study and review of manuscript. All authors have contributed to and approved the final version of the manuscript.

Corresponding author

Correspondence to Mukesh M. Desai.

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Ethics approval was taken from the institutional ethics committee.

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A written informed consent was taken from the guardians of the children included in the study.

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The authors affirm that the patients provided informed consent for publication of the images in Fig. 1.

Conflict of Interest

The authors declare no competing interests.

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Chougule, A., Taur, P., Gowri, V. et al. SPENCD Presenting with Evans Phenotype and Clinical Response to JAK1/2 Inhibitors—a Report of 2 Cases. J Clin Immunol 43, 331–334 (2023). https://doi.org/10.1007/s10875-022-01400-8

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  • DOI: https://doi.org/10.1007/s10875-022-01400-8

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