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Cervical myelomeningocele with CSF leakage: a case-based review

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Abstract

Background

The cystic spinal dysraphism of the cervical and upper thoracic region (CDCT) accounts for only 3.9 to 8% of spina bifida cystica lesions. The presence of external cerebrospinal fluid (CSF) leakage is infrequent and very few authors have reported about surgical complications.

Case report

We present the case of a new born diagnosed of CDCT C1-C3 with a stalk of fibrovascular tissue, CSF leakage, hydrocephalus, and type Chiari II malformation, discuss about the chosen surgical technique and the associated complications, and make a review of the literature focusing on the main aspects of CDCT.

Conclusions

The CDCT with a stalk of neuroglial and/or fibrovascular tissue originates from the dorsal surface of the spinal cord and penetrates into a cervical cystic sac. The presence of CSF leakage, hydrocephalus, and/or type Chiari II malformation can influence to decide the most appropriate surgical technique.

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Authors and Affiliations

  1. Neurosurgery Department, Hospital Regional Universitario de Málaga, Málaga, Spain

    Kevin Armas-Melián, Sara Iglesias, Bienvenido Ros & Miguel Ángel Arráez

  2. Department of Neurosurgery, Hospital Insular de Las Palmas, Plaza Doctor Pasteur s/n, 35016, Las Palmas de Gran Canaria, Spain

    Kevin Armas-Melián

  3. Radiology Department, Hospital Regional Universitario de Málaga, Málaga, Spain

    María Isabel Martínez-León

Authors
  1. Kevin Armas-Melián
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  2. Sara Iglesias
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  3. Bienvenido Ros
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  4. María Isabel Martínez-León
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  5. Miguel Ángel Arráez
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Correspondence to Kevin Armas-Melián.

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Armas-Melián, K., Iglesias, S., Ros, B. et al. Cervical myelomeningocele with CSF leakage: a case-based review. Childs Nerv Syst 36, 2615–2620 (2020). https://doi.org/10.1007/s00381-020-04743-y

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  • DOI: https://doi.org/10.1007/s00381-020-04743-y

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