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Situs inversus with levocardia, infrahepatic interruption of the inferior vena cava, and azygos continuation: a case report

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Abstract

Situs inversus incompletus is a rare congenital condition in which the major abdominal organs are reversed or mirrored from their normal positions. It is often associated with multiple congenital anomalies. We present the case of a 38-year-old woman with dyspnea and a clinical history of chronic kidney disease and kidney transplantation. Echocardiography showed a right atrial mass, and analysis of multidetector computed tomography angiography revealed the interruption of the inferior vena cava with an increase of the azygos vein and azygos continuation. These congenital malformations are often associated with deep vein thrombosis and/or pulmonary thromboembolism and explained the occurrence of dyspnea. Cardiac magnetic resonance with contrast medium confirmed the presence of the right atrial mass, the characteristics of which were attributed to interatrial thrombus, which was further confirmed by the success of thrombolytic therapy and the remission of symptoms. In conclusion, we described a case of situs inversus with levocardia in association with infrahepatic interruption of the inferior vena cava, and azygos continuation with cardiac thrombus and chronic renal failure.

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The author declares no conflict of interest.

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Authors and Affiliations

  1. Department of Radiology “Magrassi-Lanzara”, Second University of Naples, Piazza Miraglia 2, 80131, Naples, Italy

    Alessandra Del Prete

  2. IRCCS Foundation SDN, Naples, Italy

    Carlo Cavaliere

  3. Department of Radiology, AORN Cardarelli, Naples, Italy

    Francesco Di Pietto & Rosaria De Ritis

Authors
  1. Alessandra Del Prete
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  2. Carlo Cavaliere
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  3. Francesco Di Pietto
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  4. Rosaria De Ritis
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Correspondence to Alessandra Del Prete.

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Del Prete, A., Cavaliere, C., Di Pietto, F. et al. Situs inversus with levocardia, infrahepatic interruption of the inferior vena cava, and azygos continuation: a case report. Surg Radiol Anat 38, 369–371 (2016). https://doi.org/10.1007/s00276-015-1454-3

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  • DOI: https://doi.org/10.1007/s00276-015-1454-3

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