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Kongenitale lineare unilaterale Porokeratose

Congenital unilateral linear porokeratosis

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Zusammenfassung

Porokeratosen beruhen auf einer Störung der epidermalen Verhornung. Wir berichten über eine 27-jährige Frau, die seit Geburt an papulösen, linear angeordneten, hyperkeratotischen Hautveränderungen am rechten Fuß leidet. Im Laufe ihres Lebens breiteten sich die Herde über das ganze rechte Bein aus und dehnten sich über die rechte Seite des Stamms bis zum rechten Oberarm und dem Kinn aus. Die klinische Diagnose einer Porokeratosis linearis unilateralis wurde durch eine histopathologische Untersuchung bestätigt.

Abstract

Porokeratosis is a disorder of epidermal keratinization. A 27-year-old woman had papular, linearly arranged, hyperkeratotic lesions on the right foot since birth. Over the course of her life, the lesions progressed to involve the entire right leg and extended to the right side of her trunk, the right arm and chin. The clinical diagnosis of unilateral linear porokeratosis was confirmed by histopathology.

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  1. Klinik für Allergologie und Dermatologie, Universitätsklinikum RWTH Aachen, Pauwelsstr. 30, 52074, Aachen, Deutschland

    P. Sertznig, R. Wahl, C. Mühlhoff & M. Megahed

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  1. P. Sertznig
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  2. R. Wahl
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  3. C. Mühlhoff
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  4. M. Megahed
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Correspondence to P. Sertznig.

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Sertznig, P., Wahl, R., Mühlhoff, C. et al. Kongenitale lineare unilaterale Porokeratose. Hautarzt 60, 949–952 (2009). https://doi.org/10.1007/s00105-009-1872-4

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  • DOI: https://doi.org/10.1007/s00105-009-1872-4

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