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Uterus didelphys with obstructed hemivagina and contralateral multicystic dysplastic kidney

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Abstract

Müllerian anomalies are often associated with urinary tract anomalies. Herlyn–Werner–Wunderlich syndrome or obstructed hemivagina and ipsilateral renal anomaly are rare Müllerian anomaly comprising uterine didelphys, obstructed hemivagina, and ipsilateral renal anomaly. We report an unusual case of uterus didelphys with obstructed hemivagina and contralateral (not ipsilateral) multicystic dysplastic kidney. An early diagnosis is critical to prevent complications such as adhesions with subsequent infertility. A careful evaluation of the female reproductive tract may be necessary in children with not only renal aplasia but also lateral renal anomalies such as multicystic dysplastic kidney.

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References

  1. Lin PC, Bhatnagar KP, Nettleton S, et al. Female genital anomalies affecting reproduction. Fertil Steril. 2002;78:899–915.

    Article  PubMed  Google Scholar 

  2. Rackow BW, Arici A. Reproductive performance of women with Müllerian anomalies. Curr Opin Obstet Gynecol. 2007;19:229–37.

    Article  PubMed  Google Scholar 

  3. Smith NA, Laufer MR. Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome: management and followup. Fertil Steril. 2007;87:918–22.

    Article  PubMed  Google Scholar 

  4. Park NH, Park HJ, Park CS, et al. Herlyn-Werner-Wunderlich syndrome with unilateral hemivaginal obstruction, ipsilateral renal agenesis, and contralateral renal thin GBM disease: a case report with radiological follow up. J Korean Soc Radiol. 2010;62:383–8.

    Google Scholar 

  5. Adair L II, Georgiades M, Osborne R, et al. Uterus didelphys with unilateral distal vaginal agenesis and ipsilateral renal agenesis: common presentation of an unusual variation. J Radiol Case Rep. 2011;5:1–8.

    Article  PubMed Central  PubMed  Google Scholar 

  6. Orazi C, Lucchetti MC, Schingo PMS, et al. Herlyn-Werner-Wunderlich syndrome: uterus didelphys, blind hemivagina and ipsilateral renal agenesis. Sonographic and MR findings in 11 cases. Pediatr Radiol. 2007;37:657–65.

    Article  PubMed  Google Scholar 

  7. Arias MP, Vellibre RM, Sanchez MM, et al. Uterus didelphys with obstructed hemivagina and multicystic dysplastic kidney. Eur J Pediatr Surg. 2005;15:441–5.

    Article  Google Scholar 

  8. Han B, Herndon C, Rosen M, et al. Uterine didelphys associated with obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome. Radiol Case Rep 2010;5:327.

  9. Mesrobian HG, Rushton HG, Bulas D. Unilateral renal agenesis may result from in utero regression of multicystic renal dysplasia. J Urol. 1993;150:793–4.

    CAS  PubMed  Google Scholar 

  10. Hiraoka M, Tsukahara H, Ohshima Y, et al. Renal aplasia is the predominant cause of congenital solitary kidneys. Kidney Int. 2002;61:1840–4.

    Article  PubMed  Google Scholar 

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Conflict of interest

The authors report no conflicts of interest. The authors also declare that they have no financial associations to disclose in the drafting of this manuscript.

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Authors and Affiliations

  1. Department of Pediatrics, Institute of Medical Pharmaceutical, and Health Sciences, School of Medicine, Kanazawa University, 13-1 Takaramachi, Kanazawa, 920-8641, Japan

    Masaki Shimizu & Akihiro Yachie

  2. Department of Pediatric Surgery, Institute of Medical Pharmaceutical, and Health Sciences, School of Medicine, Kanazawa University, Kanazawa, Japan

    Seisho Sakai & Masatoshi Miyamoto

  3. Department of Pediatrics, Kanazawa Medical Center, Kanazawa, Japan

    Kazuhide Ohta

Authors
  1. Masaki Shimizu
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  2. Seisho Sakai
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  3. Kazuhide Ohta
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  4. Masatoshi Miyamoto
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  5. Akihiro Yachie
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Corresponding author

Correspondence to Masaki Shimizu.

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Shimizu, M., Sakai, S., Ohta, K. et al. Uterus didelphys with obstructed hemivagina and contralateral multicystic dysplastic kidney. CEN Case Rep 4, 61–64 (2015). https://doi.org/10.1007/s13730-014-0139-9

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  • DOI: https://doi.org/10.1007/s13730-014-0139-9

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