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Morbus Hirschsprung

  • Udo Rolle
Living reference work entry
Part of the Springer Reference Medizin book series (SRM)

Zusammenfassung

Der Morbus Hirschsprung (Megacolon congenitum) ist eine angeborene Innervationsstörung des Darms, die vom Neugeborenen- bis Kleinkindesalter durch eine funktionelle Obstruktion auffällig wird. Der klar definierte Defekt der intrinsischen Innervation lässt sich standardisiert durch Bildgebung, Funktionsdiagnostik und Histologie sichern. Eine operative Therapie dieser Erkrankung ist erforderlich. Zusätzlich bedürfen die betroffenen Kinder einer langfristigen Betreuung aufgrund häufig anhaltender Funktionsstörungen des gesamten Darms.

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Copyright information

© © Springer-Verlag GmbH Deutschland 2018

Authors and Affiliations

  1. 1.Department of Pediatric Surgery and Pediatric UrologyGoethe University FrankfurtFrankfurtDeutschland

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