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Kinderchirurgie pp 1–25Cite as

Morbus Hirschsprung

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Zusammenfassung

Der Morbus Hirschsprung (Megacolon congenitum) ist eine angeborene Innervationsstörung des Darms, die vom Neugeborenen- bis Kleinkindesalter durch eine funktionelle Obstruktion auffällig wird. Der klar definierte Defekt der intrinsischen Innervation lässt sich standardisiert durch Bildgebung, Funktionsdiagnostik und Histologie sichern. Eine operative Therapie dieser Erkrankung ist erforderlich. Zusätzlich bedürfen die betroffenen Kinder einer langfristigen Betreuung aufgrund häufig anhaltender Funktionsstörungen des gesamten Darms.

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Author information

Authors and Affiliations

  1. Department of Pediatric Surgery and Pediatric Urology, Goethe University Frankfurt, Frankfurt, Deutschland

    Udo Rolle

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  1. Udo Rolle
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Correspondence to Udo Rolle .

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Editors and Affiliations

  1. Kinderchirurgische Klinik und Poliklinik, Klinikum der Universität München Kinderchirurgische Klinik und Poliklinik, München, Bayern, Germany

    Dietrich von Schweinitz

  2. Abt. Kinderchirurgie, Medizinische Hochschule Hannover (MHH) Kinderklinik, Hannover, Germany

    Benno Ure

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Rolle, U. (2018). Morbus Hirschsprung. In: von Schweinitz, D., Ure, B. (eds) Kinderchirurgie. Springer Reference Medizin. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-53390-1_51-1

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  • DOI: https://doi.org/10.1007/978-3-662-53390-1_51-1

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  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-662-53390-1

  • Online ISBN: 978-3-662-53390-1

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